diff --git a/docs/collections.md b/docs/collections.md index 0d1ef271e..66ae89a85 100644 --- a/docs/collections.md +++ b/docs/collections.md @@ -8,12 +8,14 @@ were mainly created using the Python library [pyphetools](https://github.com/mon | Cohort | Comments |:----------- |:-------------------- | | [ANKH](https://github.com/monarch-initiative/phenopacket-store/blob/main/notebooks/ANKH/ANKH_Summary.ipynb){:target="_blank"} | 7 Phenopackets; [Craniometaphyseal dysplasia](https://omim.org/entry/123000){:target="_blank"}; [Chondrocalcinosis 2](https://omim.org/entry/118600){:target="_blank"} | +| ANKRD11 | 328 phenopackets; [KBG syndrome](https://omim.org/entry/ 148050){:target="_blank"} | | [COL3A1](https://github.com/monarch-initiative/phenopacket-store/blob/main/notebooks/COL3A1/COL3A1_Summary.ipynb){:target="_blank"} | 39 Phenopackets; [Polymicrogyria with or without vascular-type EDS](https://omim.org/entry/618343){:target="_blank"}; [Ehlers-Danlos syndrome, vascular type](https://omim.org/entry/130050){:target="_blank"} | | [ERI1](https://github.com/monarch-initiative/phenopacket-store/blob/main/notebooks/ERI1/ERI1_Guo_2013_PMID_37352860.ipynb){:target="_blank"} | 10 Phenopackets; [ERI1](https://omim.org/entry/608739){:target="_blank"} | | [EZH1](https://github.com/monarch-initiative/phenopacket-store/blob/main/notebooks/EZH1/GraciaDiaz_EZH1_PMID_37433783.ipynb){:target="_blank"} | 19 Phenopackets; [EZH1](https://omim.org/entry/601674) | -| [FBN1](https://github.com/monarch-initiative/phenopacket-store/tree/main/notebooks/FBN1){:target="_blank"} | 103 phenopackets ;[Ectopia lentis, familial](https://omim.org/entry/129600){:target="_blank"}, [Marfan lipodystrophy syndrome](https://omim.org/entry/616914){:target="_blank"}, [Marfan syndrome](https://omim.org/entry/154700){:target="_blank"}, [Geleophysic dysplasia 2](https://omim.org/entry/614185){:target="_blank"},[Acromicric dysplasia](https://omim.org/entry/102370){:target="_blank"}, | -| [FLXB4](https://github.com/monarch-initiative/phenopacket-store/tree/main/notebooks/FBXL4){:target="_blank"}| todo | +| [FBN1](https://github.com/monarch-initiative/phenopacket-store/tree/main/notebooks/FBN1){:target="_blank"} | 103 phenopackets ;[Ectopia lentis, familial](https://omim.org/entry/129600){:target="_blank"}, [Marfan lipodystrophy syndrome](https://omim.org/entry/616914){:target="_blank"}, [Marfan syndrome](https://omim.org/entry/154700){:target="_blank"}, [Geleophysic dysplasia 2](https://omim.org/entry/614185){:target="_blank"},[Acromicric dysplasia](https://omim.org/entry/102370){:target="_blank"} | +| [FLXB4](https://github.com/monarch-initiative/phenopacket-store/tree/main/notebooks/FBXL4){:target="_blank"|todo | | [GLI3](https://github.com/monarch-initiative/phenopacket-store/tree/main/notebooks/GLI3){:target="_blank"} | 77 phenopackets; [Greig cephalopolysyndactyly syndrome](https://omim.org/entry/175700){:target="_blank"}, [Pallister-Hall syndrome](https://omim.org/entry/146510){:target="_blank"}, [Polydactyly, postaxial, types A1 and B](https://omim.org/entry/174200){:target="_blank"} | +| [KDM6B](https://github.com/monarch-initiative/phenopacket-store/blob/main/notebooks/KDM6B/KDM6B_PMID_37196654.ipynb){:target="_blank"} |73 phenopackets; [Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities](https://omim.org/entry/ 618505){:target="_blank"} | diff --git a/docs/developers.md b/docs/developers.md index b0c81178d..20d9dcf74 100644 --- a/docs/developers.md +++ b/docs/developers.md @@ -15,5 +15,5 @@ other software, and then we present a notebook that summarizes the phenopackets. All phenopackets are stored in subfolders of the notebooks folder, which is organized according to cohort. phenopacket-store has a small python package that facilitates exporting all available phenopackets. See -[](https://github.com/monarch-initiative/phenopacket-store/blob/main/GetPhenopackets.ipynb){:target="_blank"} for details. +[GetPhenopackets](https://github.com/monarch-initiative/phenopacket-store/blob/main/GetPhenopackets.ipynb){:target="_blank"} for details. diff --git a/notebooks/ANKRD11/Martinez-Cayuelas-KBG-2022.ipynb b/notebooks/ANKRD11/Martinez-Cayuelas-KBG-2022.ipynb index 1ef5a0fcc..96a9da1d6 100644 --- a/notebooks/ANKRD11/Martinez-Cayuelas-KBG-2022.ipynb +++ b/notebooks/ANKRD11/Martinez-Cayuelas-KBG-2022.ipynb @@ -957,31 +957,362 @@ }, { "cell_type": "code", - "execution_count": 12, + "execution_count": 13, "id": "78e49976-d007-4819-9010-fb6756424773", "metadata": {}, "outputs": [ { - "ename": "TypeError", - "evalue": "PhenopacketTable.__init__() got an unexpected keyword argument 'phenopacket_list'", - "output_type": "error", - "traceback": [ - "\u001b[0;31m---------------------------------------------------------------------------\u001b[0m", - "\u001b[0;31mTypeError\u001b[0m Traceback (most recent call last)", - "Cell \u001b[0;32mIn[12], line 2\u001b[0m\n\u001b[1;32m 1\u001b[0m phenopackets \u001b[38;5;241m=\u001b[39m [i\u001b[38;5;241m.\u001b[39mto_ga4gh_phenopacket(metadata\u001b[38;5;241m=\u001b[39mmetadata\u001b[38;5;241m.\u001b[39mto_ga4gh()) \u001b[38;5;28;01mfor\u001b[39;00m i \u001b[38;5;129;01min\u001b[39;00m individuals]\n\u001b[0;32m----> 2\u001b[0m table \u001b[38;5;241m=\u001b[39m \u001b[43mPhenopacketTable\u001b[49m\u001b[43m(\u001b[49m\u001b[43mphenopacket_list\u001b[49m\u001b[38;5;241;43m=\u001b[39;49m\u001b[43mphenopackets\u001b[49m\u001b[43m)\u001b[49m\n\u001b[1;32m 3\u001b[0m display(HTML(table\u001b[38;5;241m.\u001b[39mto_html()))\n", - "\u001b[0;31mTypeError\u001b[0m: PhenopacketTable.__init__() got an unexpected keyword argument 'phenopacket_list'" - ] + "data": { + "text/html": [ + "
Individual | Disease | Genotype | Phenotypic features |
---|---|---|---|
KBG1 (MALE; P1Y) | KBG syndrome (OMIM:148050) | 16q24.3(89336307_89354085)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); excluded: Abnormality of the outer ear (HP:0000356) |
KBG2 (MALE; P1Y) | KBG syndrome (OMIM:148050) | 16q24.3(89256478_89506223)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); excluded: Global developmental delay (HP:0001263); excluded: Long philtrum (HP:0000343) |
KBG3 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2398_2401del (heterozygous) | Global developmental delay (HP:0001263); Thick eyebrow (HP:0000574); Hearing impairment (HP:0000365); excluded: Long philtrum (HP:0000343) |
KBG4 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7083del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); excluded: Abnormal external nose morphology (HP:0010938); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322); excluded: Hearing impairment (HP:0000365) |
KBG5 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | excluded: Long philtrum (HP:0000343) |
KBG64 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7407C>G (heterozygous) | Intellectual disability (HP:0001249); Short stature (HP:0004322); Hearing impairment (HP:0000365) |
KBG6 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6691dup (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729) |
KBG10A (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3590_3594del (heterozygous) | Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Hearing impairment (HP:0000365); excluded: Short stature (HP:0004322) |
KBG10B (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3590_3594del (heterozygous) | Macrodontia (HP:0001572); Triangular face (HP:0000325); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); excluded: Abnormal external nose morphology (HP:0010938); excluded: Thick eyebrow (HP:0000574); excluded: Long philtrum (HP:0000343); excluded: Short stature (HP:0004322) |
KBG8A (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6792dup (heterozygous) | Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Autistic behavior (HP:0000729); excluded: Thick eyebrow (HP:0000574); excluded: Long philtrum (HP:0000343); excluded: Hearing impairment (HP:0000365) |
KBG8B (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6792dup (heterozygous) | Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Thick eyebrow (HP:0000574); excluded: Long philtrum (HP:0000343) |
KBG9 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | 16q24.3(88854757_89520963)x1 (hg19): chromosomal_deletion (SO:1000029) | excluded: Intellectual disability (HP:0001249); excluded: Autistic behavior (HP:0000729); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Global developmental delay (HP:0001263); excluded: Abnormal external nose morphology (HP:0010938); excluded: Triangular face (HP:0000325); excluded: Thick eyebrow (HP:0000574); excluded: Long philtrum (HP:0000343); excluded: Abnormality of the outer ear (HP:0000356); excluded: Abnormality of the hand (HP:0001155); excluded: Hearing impairment (HP:0000365) |
KBG39 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3193A>T (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Short stature (HP:0004322); excluded: Hearing impairment (HP:0000365) |
KBG40 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3309dup (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263) |
KBG41 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1381_1384del (heterozygous) | Hearing impairment (HP:0000365) |
KBG32 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2765_2766del (heterozygous) | Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); excluded: Intellectual disability (HP:0001249); excluded: Long philtrum (HP:0000343); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322); excluded: Hearing impairment (HP:0000365) |
KBG33 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.548_551del (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Triangular face (HP:0000325); excluded: Long philtrum (HP:0000343); excluded: Short stature (HP:0004322) |
KBG34 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.831del (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Hearing impairment (HP:0000365); excluded: Abnormality of the outer ear (HP:0000356); excluded: Short stature (HP:0004322) |
KBG35 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Attention deficit hyperactivity disorder (HP:0007018); Abnormal external nose morphology (HP:0010938); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Long philtrum (HP:0000343); excluded: Short stature (HP:0004322) |
KBG36 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2408_2412del (heterozygous) | Intellectual disability (HP:0001249); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); excluded: Global developmental delay (HP:0001263); excluded: Long philtrum (HP:0000343); excluded: Abnormality of the hand (HP:0001155) |
KBG37 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3046del (heterozygous) | Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); excluded: Autistic behavior (HP:0000729); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Thick eyebrow (HP:0000574) |
KBG38 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | 16q24.3(89349711_89607741)x1 (hg19): chromosomal_deletion (SO:1000029) | Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Hearing impairment (HP:0000365); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Abnormality of the outer ear (HP:0000356); excluded: Short stature (HP:0004322) |
KBG65 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3905_3906del (heterozygous) | Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); excluded: Intellectual disability (HP:0001249); excluded: Autistic behavior (HP:0000729); excluded: Macrodontia (HP:0001572); excluded: Short stature (HP:0004322); excluded: Hearing impairment (HP:0000365) |
KBG66 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4384dup (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); excluded: Abnormality of the outer ear (HP:0000356); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
KBG59 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1731dup (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Hearing impairment (HP:0000365); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Abnormality of the outer ear (HP:0000356); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
KBG7 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1940_1941delinsT (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Macrodontia (HP:0001572); excluded: Triangular face (HP:0000325); excluded: Thick eyebrow (HP:0000574) |
KBG49 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7180C>T (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Long philtrum (HP:0000343) |
KBG50 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7570_7572del (heterozygous) | Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); excluded: Intellectual disability (HP:0001249); excluded: Short stature (HP:0004322); excluded: Hearing impairment (HP:0000365) |
KBG63 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6682del (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Long philtrum (HP:0000343); excluded: Abnormality of the hand (HP:0001155) |
KBG48 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Intellectual disability (HP:0001249); excluded: Autistic behavior (HP:0000729); excluded: Global developmental delay (HP:0001263) |
KBG43 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1367_1370del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); excluded: Global developmental delay (HP:0001263) |
KBG51 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.5790C>A (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Thick eyebrow (HP:0000574); excluded: Long philtrum (HP:0000343); excluded: Abnormality of the hand (HP:0001155) |
KBG52 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2593dup (heterozygous) | Intellectual disability (HP:0001249); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Autistic behavior (HP:0000729); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Macrodontia (HP:0001572); excluded: Long philtrum (HP:0000343); excluded: Hearing impairment (HP:0000365) |
KBG53 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1846G>T (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Abnormal external nose morphology (HP:0010938); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); excluded: Autistic behavior (HP:0000729); excluded: Macrodontia (HP:0001572); excluded: Triangular face (HP:0000325); excluded: Thick eyebrow (HP:0000574); excluded: Long philtrum (HP:0000343); excluded: Short stature (HP:0004322); excluded: Hearing impairment (HP:0000365) |
KBG54 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.520C>T (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Macrodontia (HP:0001572); excluded: Long philtrum (HP:0000343); excluded: Short stature (HP:0004322) |
KBG55 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6701del (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Thick eyebrow (HP:0000574); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); excluded: Abnormal external nose morphology (HP:0010938); excluded: Triangular face (HP:0000325); excluded: Long philtrum (HP:0000343); excluded: Hearing impairment (HP:0000365) |
KBG56 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2367del (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Abnormal external nose morphology (HP:0010938); excluded: Long philtrum (HP:0000343) |
KBG57 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2197C>T (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); excluded: Autistic behavior (HP:0000729); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Macrodontia (HP:0001572); excluded: Abnormal external nose morphology (HP:0010938); excluded: Triangular face (HP:0000325); excluded: Thick eyebrow (HP:0000574); excluded: Long philtrum (HP:0000343); excluded: Short stature (HP:0004322); excluded: Hearing impairment (HP:0000365) |
KBG58 (MALE; P1Y) | KBG syndrome (OMIM:148050) | 16q24.3(89283689-89579130)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); excluded: Autistic behavior (HP:0000729); excluded: Global developmental delay (HP:0001263); excluded: Triangular face (HP:0000325); excluded: Long philtrum (HP:0000343); excluded: Hearing impairment (HP:0000365) |
KBG31A (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7834G>T (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Triangular face (HP:0000325); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Macrodontia (HP:0001572) |
KBG47 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3448C>T (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Thick eyebrow (HP:0000574); Hearing impairment (HP:0000365); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Short stature (HP:0004322) |
KBG19 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4171C>T (heterozygous) | Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); excluded: Intellectual disability (HP:0001249); excluded: Autistic behavior (HP:0000729); excluded: Hearing impairment (HP:0000365) |
KBG20 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); excluded: Intellectual disability (HP:0001249); excluded: Long philtrum (HP:0000343); excluded: Hearing impairment (HP:0000365) |
KBG21 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3931C>T (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); excluded: Autistic behavior (HP:0000729); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Abnormality of the outer ear (HP:0000356); excluded: Short stature (HP:0004322); excluded: Hearing impairment (HP:0000365) |
KBG22 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | 16q24.3(89359701_89379306)x1 (hg19): chromosomal_deletion (SO:1000029) | Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Intellectual disability (HP:0001249); excluded: Autistic behavior (HP:0000729); excluded: Triangular face (HP:0000325); excluded: Short stature (HP:0004322) |
KBG44 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Abnormal external nose morphology (HP:0010938) |
KBG45 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); excluded: Abnormal external nose morphology (HP:0010938); excluded: Triangular face (HP:0000325); excluded: Thick eyebrow (HP:0000574); excluded: Long philtrum (HP:0000343); excluded: Short stature (HP:0004322); excluded: Hearing impairment (HP:0000365) |
KBG62 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4384dup (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Triangular face (HP:0000325); excluded: Autistic behavior (HP:0000729); excluded: Abnormal external nose morphology (HP:0010938); excluded: Thick eyebrow (HP:0000574); excluded: Long philtrum (HP:0000343); excluded: Abnormality of the outer ear (HP:0000356); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322); excluded: Hearing impairment (HP:0000365) |
KBG46 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7534C>T (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Macrodontia (HP:0001572); excluded: Abnormal external nose morphology (HP:0010938); excluded: Triangular face (HP:0000325); excluded: Thick eyebrow (HP:0000574); excluded: Abnormality of the hand (HP:0001155) |
KBG11 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3334del (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Global developmental delay (HP:0001263); excluded: Macrodontia (HP:0001572) |
KBG12 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6792dup (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Autistic behavior (HP:0000729); excluded: Triangular face (HP:0000325); excluded: Long philtrum (HP:0000343) |
KBG13 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2329_2332del (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Abnormality of the hand (HP:0001155) |
KBG14 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.5790C>A (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Hearing impairment (HP:0000365) |
KBG15 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6968_6975del (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Hearing impairment (HP:0000365); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Abnormality of the outer ear (HP:0000356); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
KBG16 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2329_2332del (heterozygous) | Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Intellectual disability (HP:0001249); excluded: Abnormality of the hand (HP:0001155) |
KBG17 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6628G>T (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Abnormality of the hand (HP:0001155) |
KBG18 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7753C>T (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Thick eyebrow (HP:0000574); excluded: Short stature (HP:0004322); excluded: Hearing impairment (HP:0000365) |
KBG23 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | 16q24.3(89325387_89409147)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Thick eyebrow (HP:0000574); excluded: Abnormality of the hand (HP:0001155) |
KBG24 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6792dup (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); excluded: Abnormality of the outer ear (HP:0000356); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322); excluded: Hearing impairment (HP:0000365) |
KBG25 (MALE; P1Y) | KBG syndrome (OMIM:148050) | 16q24.3(89556618_89557004)x1 (hg19): chromosomal_deletion (SO:1000029) | Macrodontia (HP:0001572); Thick eyebrow (HP:0000574); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Intellectual disability (HP:0001249); excluded: Autistic behavior (HP:0000729); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Abnormal external nose morphology (HP:0010938); excluded: Triangular face (HP:0000325); excluded: Long philtrum (HP:0000343); excluded: Hearing impairment (HP:0000365) |
KBG26 (MALE; P1Y) | KBG syndrome (OMIM:148050) | 16q24.3(89261399_89419131)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Triangular face (HP:0000325); excluded: Thick eyebrow (HP:0000574); excluded: Long philtrum (HP:0000343); excluded: Abnormality of the outer ear (HP:0000356); excluded: Abnormality of the hand (HP:0001155) |
KBG27 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); excluded: Thick eyebrow (HP:0000574); excluded: Abnormality of the hand (HP:0001155); excluded: Hearing impairment (HP:0000365) |
KBG28 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4529dup (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Abnormality of the outer ear (HP:0000356); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
KBG29 (MALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3704_3707del (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); excluded: Autistic behavior (HP:0000729); excluded: Triangular face (HP:0000325); excluded: Thick eyebrow (HP:0000574); excluded: Abnormality of the hand (HP:0001155); excluded: Hearing impairment (HP:0000365) |
KBG30 (FEMALE; P1Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.866dup (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); excluded: Autistic behavior (HP:0000729); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Triangular face (HP:0000325); excluded: Thick eyebrow (HP:0000574); excluded: Short stature (HP:0004322); excluded: Hearing impairment (HP:0000365) |
Alves, 2019 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.5145C>G (heterozygous) | Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365) |
Behnert, 2018 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(88854757_89577705)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Attention deficit hyperactivity disorder (HP:0007018) |
Bianchi, 2018 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2408_2412del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Hearing impairment (HP:0000365); excluded: Abnormality of the outer ear (HP:0000356); excluded: Short stature (HP:0004322) |
Bucerzan2020 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89542695_89656251)x3 (hg19): chromosomal_duplication (SO:1000037) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Crippa2015_P1 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89350931_89439639)x3 (hg19): chromosomal_duplication (SO:1000037) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Crippa2015_P2 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89350931_89439639)x3 (hg19): chromosomal_duplication (SO:1000037) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Crippa2015_P3 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89350931_89439639)x3 (hg19): chromosomal_duplication (SO:1000037) | Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155) |
Cucco, 2020 (Patient B) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3224_3227del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Hearing impairment (HP:0000365); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
DeBernardi2018 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4528_4529del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365) |
Gnazzo, 2020_P1 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1285_1286del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155) |
Gnazzo, 2020_P10 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2398_2401del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Gnazzo, 2020_P11 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2408_2412del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155) |
Gnazzo, 2020_P12 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2412del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Short stature (HP:0004322); excluded: Abnormality of the hand (HP:0001155) |
Gnazzo, 2020_P13 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3019C>T (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Gnazzo, 2020_P14 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3180dup (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); excluded: Macrodontia (HP:0001572); excluded: Abnormality of the hand (HP:0001155) |
Gnazzo, 2020_P15 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3309dup (heterozygous) | Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Short stature (HP:0004322); excluded: Intellectual disability (HP:0001249); excluded: Macrodontia (HP:0001572); excluded: Abnormality of the hand (HP:0001155) |
Gnazzo, 2020_P16 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3770_3771del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Gnazzo, 2020_P17 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4107_4108del (heterozygous) | Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); excluded: Macrodontia (HP:0001572); excluded: Abnormality of the hand (HP:0001155) |
Gnazzo, 2020_P18 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4374_4375del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Gnazzo, 2020_P19 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4389_4390del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); excluded: Macrodontia (HP:0001572); excluded: Abnormality of the hand (HP:0001155) |
Gnazzo, 2020_P2 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1385_1388del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155) |
Gnazzo, 2020_P20 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4498C>T (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Gnazzo, 2020_P21 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.5146G>T (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Gnazzo, 2020_P22 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.5205del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Gnazzo, 2020_P23 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.5712_5713insT (heterozygous) | Macrodontia (HP:0001572); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Short stature (HP:0004322); excluded: Intellectual disability (HP:0001249); excluded: Abnormality of the hand (HP:0001155) |
Gnazzo, 2020_P24 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6513dup (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Short stature (HP:0004322); excluded: Abnormality of the hand (HP:0001155) |
Gnazzo, 2020_P25 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7000C>T (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Gnazzo, 2020_P26 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7192C>T (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Gnazzo, 2020_P27 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7216C>T (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Short stature (HP:0004322); excluded: Abnormality of the hand (HP:0001155) |
Gnazzo, 2020_P28 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7416C>G (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Macrodontia (HP:0001572) |
Gnazzo, 2020_P29 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89283689_89572450)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155) |
Gnazzo, 2020_P3 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1457C>G (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); excluded: Macrodontia (HP:0001572) |
Gnazzo, 2020_P30 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89273092_89577046)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Gnazzo, 2020_P31 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2q24.3(87652026_89507330)x1 (hg19): chromosomal_deletion (SO:1000029) | Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Short stature (HP:0004322); excluded: Abnormality of mental function (HP:0011446); excluded: Abnormality of the hand (HP:0001155) |
Gnazzo, 2020_P4 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155) |
Gnazzo, 2020_P5 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1977C>G (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155) |
Gnazzo, 2020_P6 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1977C>G (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); excluded: Macrodontia (HP:0001572) |
Gnazzo, 2020_P7 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2175_2178del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Gnazzo, 2020_P8 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2175_2178del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155) |
Gnazzo, 2020_P9 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2197C>T (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); excluded: Abnormality of the hand (HP:0001155) |
Goldenberg2016_P1 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89249149_89376186)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Short stature (HP:0004322); excluded: Abnormality of the hand (HP:0001155) |
Goldenberg2016_P10 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89199607_89472627)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Goldenberg2016_P11 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Goldenberg2016_P12 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89315698_89548093)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); excluded: Abnormality of the hand (HP:0001155) |
Goldenberg2016_P13 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(88809983_89472627)x1 (hg19): chromosomal_deletion (SO:1000029) | Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Goldenberg2016_P14 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1120G>T (heterozygous) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Goldenberg2016_P15 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3198_3199del (heterozygous) | Global developmental delay (HP:0001263); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Goldenberg2016_P16 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1381_1384del (heterozygous) | Global developmental delay (HP:0001263); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Goldenberg2016_P17 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1381_1384del (heterozygous) | Global developmental delay (HP:0001263); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Macrodontia (HP:0001572) |
Goldenberg2016_P18 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2-q24.3(88621654_89383486)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Short stature (HP:0004322); excluded: Abnormality of the hand (HP:0001155) |
Goldenberg2016_P19 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89328477_89477051)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365) |
Goldenberg2016_P2 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89249149_89376186)x1 (hg19): chromosomal_deletion (SO:1000029) | Macrodontia (HP:0001572); Short stature (HP:0004322); excluded: Abnormality of the hand (HP:0001155) |
Goldenberg2016_P20 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89328477_89477051)x1 (hg19): chromosomal_deletion (SO:1000029) | Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365) |
Goldenberg2016_P21 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89161684-89505106)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Short stature (HP:0004322); excluded: Abnormality of the hand (HP:0001155) |
Goldenberg2016_P22 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2-q24.3(88230961_89383486)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Short stature (HP:0004322) |
Goldenberg2016_P23 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3774_3775del (heterozygous) | Global developmental delay (HP:0001263); Short stature (HP:0004322); excluded: Macrodontia (HP:0001572); excluded: Abnormality of the hand (HP:0001155) |
Goldenberg2016_P24 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89435258-89553707)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Short stature (HP:0004322) |
Goldenberg2016_P25 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2647G>T (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Short stature (HP:0004322); excluded: Macrodontia (HP:0001572); excluded: Abnormality of the hand (HP:0001155) |
Goldenberg2016_P26 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2-q24.3(87925812_89521860)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); excluded: Abnormality of the hand (HP:0001155) |
Goldenberg2016_P27 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6792dup (heterozygous) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Short stature (HP:0004322); excluded: Abnormality of the hand (HP:0001155) |
Goldenberg2016_P28 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(88763460_89344049)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Goldenberg2016_P29 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89461583_89559189)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Short stature (HP:0004322); excluded: Macrodontia (HP:0001572); excluded: Abnormality of the hand (HP:0001155) |
Goldenberg2016_P3 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89249149_89376186)x1 (hg19): chromosomal_deletion (SO:1000029) | Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Goldenberg2016_P30 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6766C>T (heterozygous) | Global developmental delay (HP:0001263); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Intellectual disability (HP:0001249); excluded: Short stature (HP:0004322) |
Goldenberg2016_P31 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1367_1370del (heterozygous) | Global developmental delay (HP:0001263); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Goldenberg2016_P32 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(87800226-89559330)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Abnormality of the hand (HP:0001155) |
Goldenberg2016_P33 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89507776_89565656)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Macrodontia (HP:0001572) |
Goldenberg2016_P34 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4087C>T (heterozygous) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Goldenberg2016_P35 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4786G>T (heterozygous) | Global developmental delay (HP:0001263); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Short stature (HP:0004322) |
Goldenberg2016_P36 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89295307_89559189)x1 (hg19): chromosomal_deletion (SO:1000029) | Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Short stature (HP:0004322) |
Goldenberg2016_P38 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.867C>G (heterozygous) | Macrodontia (HP:0001572); Short stature (HP:0004322); excluded: Abnormality of the hand (HP:0001155) |
Goldenberg2016_P39 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1893dup (heterozygous) | Abnormality of the hand (HP:0001155); excluded: Macrodontia (HP:0001572); excluded: Short stature (HP:0004322) |
Goldenberg2016_P4 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89249149_89376186)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Goldenberg2016_P5 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1381_1384del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Macrodontia (HP:0001572); excluded: Short stature (HP:0004322) |
Goldenberg2016_P6 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3153del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Goldenberg2016_P7 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3045del (heterozygous) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Intellectual disability (HP:0001249); excluded: Short stature (HP:0004322) |
Goldenberg2016_P8 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2398_2401del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Goldenberg2016_P9 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Global developmental delay (HP:0001263); Abnormality of the hand (HP:0001155); excluded: Macrodontia (HP:0001572); excluded: Short stature (HP:0004322) |
Isrie, 2012_P1 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89343893_89565656)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365) |
Isrie, 2012_P2 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89335228-89472768)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Thick eyebrow (HP:0000574); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Abnormality of the hand (HP:0001155) |
Jin Kim, 2020_P1 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.5889del (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365) |
Jin Kim, 2020_P2 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3310dup (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Macrodontia (HP:0001572); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Khalifa, 2013_P1A (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89388113_89541926)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Triangular face (HP:0000325) |
Khalifa, 2013_P1B (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89388113_89541926)x1 (hg19): chromosomal_deletion (SO:1000029) | Macrodontia (HP:0001572); Long philtrum (HP:0000343); excluded: Autistic behavior (HP:0000729); excluded: Triangular face (HP:0000325); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322); excluded: Hearing impairment (HP:0000365) |
Kim, 2015_P1 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2398_2401del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); excluded: Abnormality of the hand (HP:0001155) |
Kim, 2015_P2 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2398_2401del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); excluded: Abnormality of the hand (HP:0001155) |
Kim, 2015_P3 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2398_2401del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Kleyner, 2016 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6015dup (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Triangular face (HP:0000325) |
Kutkowska-Kazmierczak2021_P1 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Triangular face (HP:0000325); Short stature (HP:0004322); excluded: Intellectual disability (HP:0001249) |
Kutkowska-Kazmierczak2021_P10 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3295_3296del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Triangular face (HP:0000325); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P11 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3771dup (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P12 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1385_1388del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); excluded: Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P13 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6053_6057del (heterozygous) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Triangular face (HP:0000325); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P14 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2-24.3(87954851-89484166)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); excluded: Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P15 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89238120-89341161)x1 (hg19): chromosomal_deletion (SO:1000029) | excluded: Macrodontia (HP:0001572); excluded: Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P16 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89343893-89584394)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); excluded: Macrodontia (HP:0001572); excluded: Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P17 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89261814-89556020)x3 (hg19): chromosomal_duplication (SO:1000037) | Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); excluded: Intellectual disability (HP:0001249); excluded: Macrodontia (HP:0001572); excluded: Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P18 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89332453-89371851)x1 (hg19): chromosomal_deletion (SO:1000029) | excluded: Intellectual disability (HP:0001249); excluded: Macrodontia (HP:0001572); excluded: Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P19 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89343893-89497947)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); excluded: Macrodontia (HP:0001572); excluded: Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P2 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); excluded: Intellectual disability (HP:0001249); excluded: Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P20 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89525403-89553574)x1 (hg19): chromosomal_deletion (SO:1000029) | Short stature (HP:0004322); excluded: Macrodontia (HP:0001572) |
Kutkowska-Kazmierczak2021_P21 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89547555-89556020)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P22 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89476167-89484721)x1 (hg19): chromosomal_deletion (SO:1000029) | Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); excluded: Macrodontia (HP:0001572); excluded: Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P23 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89343893-89555548)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P3 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7607G>A (heterozygous) | Triangular face (HP:0000325); excluded: Intellectual disability (HP:0001249); excluded: Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P4 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4558del (heterozygous) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Triangular face (HP:0000325); Short stature (HP:0004322); excluded: Intellectual disability (HP:0001249) |
Kutkowska-Kazmierczak2021_P5 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2395A>T (heterozygous) | Global developmental delay (HP:0001263); Triangular face (HP:0000325); excluded: Intellectual disability (HP:0001249); excluded: Macrodontia (HP:0001572); excluded: Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P6 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1389dup (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Triangular face (HP:0000325); Short stature (HP:0004322); excluded: Macrodontia (HP:0001572) |
Kutkowska-Kazmierczak2021_P7 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7552C>T (heterozygous) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P8 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2828_2829del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Triangular face (HP:0000325); excluded: Short stature (HP:0004322) |
Kutkowska-Kazmierczak2021_P9 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6340C>T (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); excluded: Short stature (HP:0004322) |
Libianto2019 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3045del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Triangular face (HP:0000325); excluded: Long philtrum (HP:0000343) |
Lim2014 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89349966-89593853)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); excluded: Abnormality of the hand (HP:0001155) |
Low, 2016_30 (28) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4408A>T (heterozygous) | Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365) |
Low, 2016_31 (29) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2182_2183del (heterozygous) | Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); excluded: Abnormality of the hand (HP:0001155) |
Low, 2016_32 (30) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2182_2183del (heterozygous) | Macrodontia (HP:0001572); excluded: Abnormality of mental function (HP:0011446); excluded: Abnormality of the hand (HP:0001155) |
Low, 2016_33 (31) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2182_2183del (heterozygous) | Macrodontia (HP:0001572); Hearing impairment (HP:0000365); excluded: Abnormality of mental function (HP:0011446); excluded: Abnormality of the hand (HP:0001155) |
Low, 2016_34 (32) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2512C>T (heterozygous) | Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Abnormality of mental function (HP:0011446) |
Low, 2016_P1 (19) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Macrodontia (HP:0001572); Short stature (HP:0004322); excluded: Abnormality of mental function (HP:0011446); excluded: Abnormality of the hand (HP:0001155) |
Low, 2016_P10 (18) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2408_2412del (heterozygous) | Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Abnormality of mental function (HP:0011446) |
Low, 2016_P11 (20) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2408_2412del (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155) |
Low, 2016_P12 (13) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2408_2412del (heterozygous) | Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); excluded: Abnormality of mental function (HP:0011446) |
Low, 2016_P13 (27) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2408_2412del (heterozygous) | Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Abnormality of mental function (HP:0011446) |
Low, 2016_P14 (2) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2398_2401del (heterozygous) | Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Abnormality of mental function (HP:0011446) |
Low, 2016_P15 (3) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.5426_5430del (heterozygous) | Macrodontia (HP:0001572); Hearing impairment (HP:0000365); excluded: Abnormality of mental function (HP:0011446); excluded: Abnormality of the hand (HP:0001155) |
Low, 2016_P16 (9) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.5274dup (heterozygous) | Autistic behavior (HP:0000729); Macrodontia (HP:0001572); excluded: Abnormality of the hand (HP:0001155) |
Low, 2016_P17 (10) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3437_3461del (heterozygous) | Macrodontia (HP:0001572); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Abnormality of mental function (HP:0011446); excluded: Abnormality of the hand (HP:0001155) |
Low, 2016_P18 (12) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1381_1384del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Hearing impairment (HP:0000365); excluded: Abnormality of the hand (HP:0001155) |
Low, 2016_P2 (26) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Abnormality of the hand (HP:0001155); excluded: Abnormality of mental function (HP:0011446); excluded: Macrodontia (HP:0001572) |
Low, 2016_P20 (14) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4103_4104del (heterozygous) | Macrodontia (HP:0001572); Hearing impairment (HP:0000365); excluded: Abnormality of mental function (HP:0011446); excluded: Abnormality of the hand (HP:0001155) |
Low, 2016_P21 (15) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7363del (heterozygous) | Macrodontia (HP:0001572); Hearing impairment (HP:0000365); excluded: Abnormality of mental function (HP:0011446); excluded: Abnormality of the hand (HP:0001155) |
Low, 2016_P22 (16) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3208_3209del (heterozygous) | Macrodontia (HP:0001572); Hearing impairment (HP:0000365); excluded: Abnormality of mental function (HP:0011446); excluded: Abnormality of the hand (HP:0001155) |
Low, 2016_P23 (17) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4177_4189del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155) |
Low, 2016_P24 (21) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3582del (heterozygous) | Macrodontia (HP:0001572); excluded: Abnormality of mental function (HP:0011446); excluded: Abnormality of the hand (HP:0001155) |
Low, 2016_P25 (22) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3704_3707del (heterozygous) | excluded: Abnormality of mental function (HP:0011446); excluded: Macrodontia (HP:0001572); excluded: Abnormality of the hand (HP:0001155) |
Low, 2016_P26 (23) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4206C>G (heterozygous) | Autistic behavior (HP:0000729); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365) |
Low, 2016_P27 (24) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.5199_5227del (heterozygous) | Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Abnormality of mental function (HP:0011446) |
Low, 2016_P28 (25) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6364_6367del (heterozygous) | Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Hearing impairment (HP:0000365); excluded: Abnormality of the hand (HP:0001155) |
Low, 2016_P29 (27) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1801C>T (heterozygous) | Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Abnormality of mental function (HP:0011446) |
Low, 2016_P3 (4) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Macrodontia (HP:0001572); excluded: Abnormality of mental function (HP:0011446); excluded: Abnormality of the hand (HP:0001155) |
Low, 2016_P4 (5) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Abnormality of mental function (HP:0011446) |
Low, 2016_P5 (6) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Abnormality of mental function (HP:0011446) |
Low, 2016_P6 (7) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); excluded: Abnormality of mental function (HP:0011446) |
Low, 2016_P7 (8) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); excluded: Abnormality of mental function (HP:0011446) |
Low, 2016_P8 (33) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | excluded: Abnormality of mental function (HP:0011446); excluded: Macrodontia (HP:0001572); excluded: Abnormality of the hand (HP:0001155) |
Low, 2016_P9 (1) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2408_2412del (heterozygous) | Autistic behavior (HP:0000729); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Macrodontia (HP:0001572) |
Low2017 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7471-1G>C (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Hearing impairment (HP:0000365) |
Mattei2021 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Hearing impairment (HP:0000365); excluded: Abnormality of the outer ear (HP:0000356); excluded: Short stature (HP:0004322) |
Miyatake, 2013 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2-q24.3(88641808-89332049)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); excluded: Autistic behavior (HP:0000729); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Triangular face (HP:0000325); excluded: Short stature (HP:0004322) |
Miyatake, 2017_P1 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Macrodontia (HP:0001572); excluded: Abnormal external nose morphology (HP:0010938) |
Miyatake, 2017_P2 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3224_3227del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155); excluded: Triangular face (HP:0000325) |
Miyatake, 2017_P3 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6187G>T (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); excluded: Abnormal external nose morphology (HP:0010938); excluded: Abnormality of the hand (HP:0001155) |
Murray, 2017_P1 (1.1) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Triangular face (HP:0000325); Long philtrum (HP:0000343); Hearing impairment (HP:0000365); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Murray, 2017_P10 (7.1.) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7471A>C (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Murray, 2017_P11 (8.1.) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6409_6410del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Murray, 2017_P12 (9.1) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3224_3227del (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Murray, 2017_P13 (11.1) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7216C>T (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Murray, 2017_P16 (13.1) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6472G>T (heterozygous) | Intellectual disability (HP:0001249); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365) |
Murray, 2017_P2 (1.2) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Murray, 2017_P3 (1.3) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); excluded: Abnormality of the outer ear (HP:0000356); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Murray, 2017_P4 (2.1) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.505G>T (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Murray, 2017_P5 (3.1) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4406G>A (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155); excluded: Long philtrum (HP:0000343); excluded: Short stature (HP:0004322) |
Murray, 2017_P6 (3.2) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4406G>A (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Triangular face (HP:0000325); excluded: Long philtrum (HP:0000343) |
Murray, 2017_P7 (3.3) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4406G>A (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Long philtrum (HP:0000343) |
Murray, 2017_P8 (4.1) (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Intellectual disability (HP:0001249); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365) |
Murray, 2017_P9 (5.1.) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1173C>G (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); excluded: Abnormality of the outer ear (HP:0000356); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Novara, 2017_P1 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2-q24.3 (88635000_89628950)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Triangular face (HP:0000325) |
Novara, 2017_P11 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3 (89161684_89505106)x1 (hg19): chromosomal_deletion (SO:1000029) | Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Novara, 2017_P12 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2-q24.3(88666177_89472627)x1 (hg19): chromosomal_deletion (SO:1000029) | Long philtrum (HP:0000343); Hearing impairment (HP:0000365); excluded: Triangular face (HP:0000325); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Novara, 2017_P2 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2-q24.3 (87340135_89335428)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Abnormality of the hand (HP:0001155); excluded: Macrodontia (HP:0001572); excluded: Triangular face (HP:0000325); excluded: Short stature (HP:0004322) |
Novara, 2017_P3 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2-q24.3 (88230961_89363602)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Hearing impairment (HP:0000365); excluded: Triangular face (HP:0000325); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Novara, 2017_P4 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2-q24.3 (88755312_89584412)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); excluded: Triangular face (HP:0000325); excluded: Thick eyebrow (HP:0000574); excluded: Abnormality of the hand (HP:0001155) |
Novara, 2017_P5 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2-q24.3 (88556191_89557911)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Hearing impairment (HP:0000365); excluded: Triangular face (HP:0000325); excluded: Thick eyebrow (HP:0000574); excluded: Abnormality of the outer ear (HP:0000356); excluded: Short stature (HP:0004322) |
Novara, 2017_P7 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2-q24.3 (88230760-89363742)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); excluded: Triangular face (HP:0000325); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Novara, 2017_P8 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2-q24.3 (88630607_89607742)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729) |
Novara, 2017_P9 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2-q24.3 (87183661_89520803)x1 (hg19): chromosomal_deletion (SO:1000029) | Short stature (HP:0004322) |
Ockeloen2015_P1 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7481dup (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Ockeloen2015_P10 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Ockeloen2015_P11 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3832A>T (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Ockeloen2015_P12 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3832A>T (heterozygous) | Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Ockeloen2015_P13 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3832A>T (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Ockeloen2015_P14 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2751dup (heterozygous) | Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Short stature (HP:0004322); excluded: Intellectual disability (HP:0001249); excluded: Abnormality of the hand (HP:0001155) |
Ockeloen2015_P15 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3382_3383del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365) |
Ockeloen2015_P16 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Ockeloen2015_P17 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6513dup (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365) |
Ockeloen2015_P18 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1318C>T (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Ockeloen2015_P19 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1318C>T (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Ockeloen2015_P2 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7481dup (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Ockeloen2015_P20 (UNKNOWN; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(88231090-89388103)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Short stature (HP:0004322); excluded: Triangular face (HP:0000325); excluded: Abnormality of the hand (HP:0001155) |
Ockeloen2015_P3 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7481dup (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Short stature (HP:0004322) |
Ockeloen2015_P4 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7481dup (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Triangular face (HP:0000325) |
Ockeloen2015_P5 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7481dup (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365) |
Ockeloen2015_P6 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4391_4392del (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Ockeloen2015_P7 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6184del (heterozygous) | Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Ockeloen2015_P8 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3123_3126del (heterozygous) | Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Intellectual disability (HP:0001249) |
Ockeloen2015_P9 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1460_1463del (heterozygous) | Intellectual disability (HP:0001249); Triangular face (HP:0000325); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Macrodontia (HP:0001572) |
Palumbo 2016 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2q24.3 (87502161_89688617)x3 (hg19): chromosomal_duplication (SO:1000037) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Abnormality of the hand (HP:0001155); excluded: Autistic behavior (HP:0000729); excluded: Short stature (HP:0004322); excluded: Hearing impairment (HP:0000365) |
Parenti2016_P1 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.5483C>A (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); excluded: Macrodontia (HP:0001572); excluded: Triangular face (HP:0000325); excluded: Short stature (HP:0004322) |
Parenti2016_P2 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2297_2300del (heterozygous) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155); excluded: Triangular face (HP:0000325); excluded: Short stature (HP:0004322) |
Parenti2021_P1 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.915del (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Hearing impairment (HP:0000365); excluded: Triangular face (HP:0000325); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Parenti2021_P10 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4218C>A (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); excluded: Triangular face (HP:0000325); excluded: Thick eyebrow (HP:0000574); excluded: Short stature (HP:0004322) |
Parenti2021_P11 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4087C>T (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); excluded: Macrodontia (HP:0001572); excluded: Triangular face (HP:0000325); excluded: Short stature (HP:0004322) |
Parenti2021_P12 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7470+2T>C (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Parenti2021_P13 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1381_1384del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Parenti2021_P14 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); excluded: Thick eyebrow (HP:0000574); excluded: Short stature (HP:0004322) |
Parenti2021_P15 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3888dup (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); excluded: Thick eyebrow (HP:0000574); excluded: Short stature (HP:0004322) |
Parenti2021_P16 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3591_3594del (heterozygous) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Short stature (HP:0004322) |
Parenti2021_P17 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1381_1384del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); excluded: Autistic behavior (HP:0000729); excluded: Global developmental delay (HP:0001263); excluded: Short stature (HP:0004322) |
Parenti2021_P18 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Short stature (HP:0004322) |
Parenti2021_P19 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Thick eyebrow (HP:0000574); excluded: Short stature (HP:0004322) |
Parenti2021_P2 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1711_1723del (heterozygous) | Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); excluded: Intellectual disability (HP:0001249); excluded: Triangular face (HP:0000325); excluded: Thick eyebrow (HP:0000574); excluded: Short stature (HP:0004322) |
Parenti2021_P20 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2408_2412del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); excluded: Thick eyebrow (HP:0000574); excluded: Short stature (HP:0004322) |
Parenti2021_P21 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.5123C>A (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Parenti2021_P22 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1381_1384del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Autistic behavior (HP:0000729); excluded: Attention deficit hyperactivity disorder (HP:0007018) |
Parenti2021_P23 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89335426-89371803)x1 (hg19): chromosomal_deletion (SO:1000029) | Autistic behavior (HP:0000729); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365) |
Parenti2021_P3 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1977C>G (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Triangular face (HP:0000325) |
Parenti2021_P4 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2398_2401del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Triangular face (HP:0000325) |
Parenti2021_P5 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2408_2412del (heterozygous) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Intellectual disability (HP:0001249); excluded: Triangular face (HP:0000325) |
Parenti2021_P6 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2692C>T (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); excluded: Triangular face (HP:0000325); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Parenti2021_P7 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7356dup (heterozygous) | Global developmental delay (HP:0001263); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); excluded: Intellectual disability (HP:0001249); excluded: Macrodontia (HP:0001572); excluded: Triangular face (HP:0000325); excluded: Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Parenti2021_P8 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7411_7422del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); excluded: Triangular face (HP:0000325); excluded: Thick eyebrow (HP:0000574); excluded: Short stature (HP:0004322) |
Parenti2021_P9 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155); excluded: Triangular face (HP:0000325); excluded: Short stature (HP:0004322) |
Rentas2021_P1 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.211_226+1del (heterozygous) | Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); excluded: Short stature (HP:0004322) |
Sacharow, 2012_P1 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89283689_89603390)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Triangular face (HP:0000325); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365); excluded: Short stature (HP:0004322) |
Sacharow, 2012_P2 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89295307-89660379)x1 (hg19): chromosomal_deletion (SO:1000029) | Macrodontia (HP:0001572); Triangular face (HP:0000325); Abnormality of the hand (HP:0001155) |
Sayed, 2020_P1 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.5488G>T (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Sayed, 2020_P2 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.5488G>T (heterozygous) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Short stature (HP:0004322); excluded: Thick eyebrow (HP:0000574); excluded: Abnormality of the hand (HP:0001155) |
Scarano, 2013_P1 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2197C>T (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Triangular face (HP:0000325); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365) |
Scarano, 2013_P10 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2-q24.3 (89283689_89429735)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Scarano, 2013_P11 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3 (89335428_89559189)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Triangular face (HP:0000325); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Scarano, 2013_P12 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3 (89429676_89559189)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Scarano, 2013_P2 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3221_3222del (heterozygous) | Macrodontia (HP:0001572); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Scarano, 2013_P3 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.5957_5958del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Scarano, 2013_P4 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3974del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365) |
Scarano, 2013_P5 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3222dup (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Triangular face (HP:0000325); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Scarano, 2013_P6 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2866G>T (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Triangular face (HP:0000325); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Scarano, 2013_P7 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7534C>T (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Scarano, 2013_P8 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2650del (heterozygous) | Macrodontia (HP:0001572); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Intellectual disability (HP:0001249) |
Scarano, 2013_P9 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3339G>A (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); Hearing impairment (HP:0000365) |
Sirmaci2011_P1/F1? (previously published Tekin, 2004) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7570-1G>C (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155) |
Sirmaci2011_P2 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2305del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155) |
Sirmaci2011_P2/F1? (previously published Tekin, 2004) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7570-1G>C (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Hearing impairment (HP:0000365) |
Sirmaci2011_P3 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7189C>T (heterozygous) | Intellectual disability (HP:0001249); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the hand (HP:0001155) |
Sirmaci2011_P3/F1? (previously published Tekin, 2004) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7570-1G>C (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155) |
Sirmaci2011_P4 (previously published Brancati, 2004) (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.5953_5954del (heterozygous) | Intellectual disability (HP:0001249); Attention deficit hyperactivity disorder (HP:0007018); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155) |
Sirmaci2011_P5 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6071_6084del (heterozygous) | Intellectual disability (HP:0001249); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155) |
Spengler, 2013 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89371838_89607414)x1 (hg19): chromosomal_deletion (SO:1000029) | Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Abnormality of the outer ear (HP:0000356); Abnormality of the hand (HP:0001155); Short stature (HP:0004322); excluded: Intellectual disability (HP:0001249) |
Srivastava, 2017_P1 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.1q24.3 (86680657_89578069)x1 (hg19): chromosomal_deletion (SO:1000029) | Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Thick eyebrow (HP:0000574); Long philtrum (HP:0000343); Short stature (HP:0004322); Hearing impairment (HP:0000365); excluded: Abnormality of the hand (HP:0001155) |
VanDongen2019_P1 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1763C>A (heterozygous) | Hearing impairment (HP:0000365) |
VanDongen2019_P10 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.3460G>T (heterozygous) | Hearing impairment (HP:0000365) |
VanDongen2019_P3 (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4964_4965del (heterozygous) | Hearing impairment (HP:0000365) |
VanDongen2019_P6 (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2175_2178del (heterozygous) | Hearing impairment (HP:0000365) |
Walz2015_PA (FEMALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1785_1786delinsTT (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Walz2015_PB (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.1903_1907del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155); Short stature (HP:0004322) |
Walz2015_PC (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.2130del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Walz2015_PD (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.4283_4286del (heterozygous) | Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Short stature (HP:0004322); excluded: Intellectual disability (HP:0001249) |
Walz2015_PE (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.6817_6833del (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Short stature (HP:0004322) |
Walz2015_Pf (MALE; P2Y) | KBG syndrome (OMIM:148050) | NM_013275.6:c.7535G>A (heterozygous) | Intellectual disability (HP:0001249); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Thick eyebrow (HP:0000574); Abnormality of the hand (HP:0001155); excluded: Short stature (HP:0004322) |
Willemsen2010_P1 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89122739_89501030)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Abnormality of the outer ear (HP:0000356); Short stature (HP:0004322); excluded: Triangular face (HP:0000325) |
Willemsen2010_P2 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(89273092_89538759)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); excluded: Abnormality of the outer ear (HP:0000356); excluded: Short stature (HP:0004322) |
Willemsen2010_P3 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2-24.3(87498264_89596942)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Global developmental delay (HP:0001263); Hearing impairment (HP:0000365); excluded: Thick eyebrow (HP:0000574); excluded: Abnormality of the outer ear (HP:0000356) |
Willemsen2010_P4 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.2-24.3(88230961_89363602)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); excluded: Abnormality of the outer ear (HP:0000356); excluded: Short stature (HP:0004322) |
Youngs2011 (MALE; P2Y) | KBG syndrome (OMIM:148050) | 16q24.3(87920000-88100000)x1 (hg19): chromosomal_deletion (SO:1000029) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Global developmental delay (HP:0001263); Macrodontia (HP:0001572); Abnormal external nose morphology (HP:0010938); Triangular face (HP:0000325); Short stature (HP:0004322); Hearing impairment (HP:0000365) |
5 rows × 77 columns
\n", + "5 rows × 76 columns
\n", "" ], "text/plain": [ @@ -516,33 +525,26 @@ "Individual 5 Heterozygous No \n", "Individual 6 Heterozygous No \n", "\n", - "Field ... \\\n", - "Individual 1 ... \n", - "Individual 2 ... \n", - "Individual 3 ... \n", - "Individual 5 ... \n", - "Individual 6 ... \n", + "Field ... Constipation \\\n", + "Individual 1 ... No \n", + "Individual 2 ... No \n", + "Individual 3 ... Yes \n", + "Individual 5 ... No \n", + "Individual 6 ... No \n", "\n", - "Field Other \\\n", + "Field Other_gi \\\n", "Individual 1 NaN \n", "Individual 2 NaN \n", "Individual 3 NaN \n", "Individual 5 Eats/drinks no cow's milk, no gluten and little soya. No allergy but seems sensitive to these products \n", "Individual 6 NaN \n", "\n", - "Field Other Skin hyperlaxity Genitourinary abnormalities \\\n", - "Individual 1 NaN No No \n", - "Individual 2 NaN No No \n", - "Individual 3 NaN No No \n", - "Individual 5 NaN No No \n", - "Individual 6 NaN No phimosis \n", - "\n", - "Field Cryptorchidism \\\n", - "Individual 1 NaN \n", - "Individual 2 NaN \n", - "Individual 3 No \n", - "Individual 5 No \n", - "Individual 6 No \n", + "Field Skin hyperlaxity Genitourinary abnormalities Cryptorchidism \\\n", + "Individual 1 No No NaN \n", + "Individual 2 No No NaN \n", + "Individual 3 No No No \n", + "Individual 5 No No No \n", + "Individual 6 No phimosis No \n", "\n", "Field Other medication received \\\n", "Individual 1 Not reported \n", @@ -572,10 +574,10 @@ "Individual 5 NaN NaN \n", "Individual 6 NaN NaN \n", "\n", - "[5 rows x 77 columns]" + "[5 rows x 76 columns]" ] }, - "execution_count": 14, + "execution_count": 5, "metadata": {}, "output_type": "execute_result" } @@ -589,7 +591,7 @@ }, { "cell_type": "code", - "execution_count": 16, + "execution_count": 6, "id": "ca522a2e-b23c-42ae-80dd-9300864d3821", "metadata": {}, "outputs": [ @@ -625,7 +627,7 @@ "5 rows × 78 columns
\n", + "5 rows × 77 columns
\n", "" ], "text/plain": [ @@ -792,19 +794,26 @@ "Individual 5 Heterozygous No \n", "Individual 6 Heterozygous No \n", "\n", - "Field ... Other Skin hyperlaxity Genitourinary abnormalities \\\n", - "Individual 1 ... NaN No No \n", - "Individual 2 ... NaN No No \n", - "Individual 3 ... NaN No No \n", - "Individual 5 ... NaN No No \n", - "Individual 6 ... NaN No phimosis \n", + "Field ... \\\n", + "Individual 1 ... \n", + "Individual 2 ... \n", + "Individual 3 ... \n", + "Individual 5 ... \n", + "Individual 6 ... \n", + "\n", + "Field Other_gi \\\n", + "Individual 1 NaN \n", + "Individual 2 NaN \n", + "Individual 3 NaN \n", + "Individual 5 Eats/drinks no cow's milk, no gluten and little soya. No allergy but seems sensitive to these products \n", + "Individual 6 NaN \n", "\n", - "Field Cryptorchidism \\\n", - "Individual 1 NaN \n", - "Individual 2 NaN \n", - "Individual 3 No \n", - "Individual 5 No \n", - "Individual 6 No \n", + "Field Skin hyperlaxity Genitourinary abnormalities Cryptorchidism \\\n", + "Individual 1 No No NaN \n", + "Individual 2 No No NaN \n", + "Individual 3 No No No \n", + "Individual 5 No No No \n", + "Individual 6 No phimosis No \n", "\n", "Field Other medication received \\\n", "Individual 1 Not reported \n", @@ -841,10 +850,10 @@ "Individual 5 NaN Individual 5 \n", "Individual 6 NaN Individual 6 \n", "\n", - "[5 rows x 78 columns]" + "[5 rows x 77 columns]" ] }, - "execution_count": 16, + "execution_count": 6, "metadata": {}, "output_type": "execute_result" } @@ -856,7 +865,7 @@ }, { "cell_type": "code", - "execution_count": 17, + "execution_count": 7, "id": "16a36bc8-1ad8-421a-ba39-8d1e45dcd9c5", "metadata": {}, "outputs": [], @@ -866,17 +875,17 @@ }, { "cell_type": "code", - "execution_count": 18, + "execution_count": 8, "id": "a6c7acc5-9486-4272-9f34-6df9190e38a8", "metadata": {}, "outputs": [], "source": [ - "column_d = generator.try_mapping_columns()" + "column_mapper_d = generator.try_mapping_columns()" ] }, { "cell_type": "code", - "execution_count": 21, + "execution_count": 9, "id": "235ca20f-294d-4506-9af2-a319d77d89c2", "metadata": {}, "outputs": [ @@ -891,7 +900,7 @@ " \n", " \n", "Sex;
Age, years;
Cohort type;
Mutation (NM_);
cDNA change (ENST00000254846.9 or NM_001080424.2);
Amino acid change;
Variant Type (PTV or PAV);
Inheritance;
Heterozygous/Homozygous;
Additional findings of genetic testing;
Other affected relatives;
Pregnancy/delivery;
Complications of Pregnancy/Delivery;
Gestational age, weeks;
Birth weight, g (SD);
Growth;
Height, cm (SD);
Weight, kg(SD);
Head circumference, cm(SD);
Age at folow-up/measurements, years;
Neurodevelopment;
Language/speech delay;
First words, months;
First steps, months;
IQ profile;
nan;
nan;
Behavior problems;
Psychosis / Schizophrenia;
Use of psychiatric drugs;
Other;
Neurological;
Seizures / Epilepsy;
Dystonia, if present - type and age of onset;
Other neurological/movement issues;
Brain MRI findings;
Musculoskeletal/extremities;
Vertebral abnormalities (Scoliosis, kyphosis etc).;
Hand /foot/ finger abnormalities;
Other;
Dysmorphism;
Dysmorphic features;
Lip/palate cleft;
Eyes/visual problems;
Hypermetropia/myopia;
Other;
Ear/ hearing problems;
Hearing;
Other;
Cardiovascular;
Congenital heart disease;
Other;
Gastrointestinal;
Neonatal feeding difficulties;
Yes;
Other;
Other;
Skin hyperlaxity;
Genitourinary abnormalities;
Other medication received;
Other;
nan;
nan;
nan;
patient_id
Sex;
Age, years;
Cohort type;
Mutation (NM_);
cDNA change (ENST00000254846.9 or NM_001080424.2);
Amino acid change;
Variant Type (PTV or PAV);
Inheritance;
Heterozygous/Homozygous;
Additional findings of genetic testing;
Other affected relatives;
Pregnancy/delivery;
Complications of Pregnancy/Delivery;
Gestational age, weeks;
Birth weight, g (SD);
Growth;
Height, cm (SD);
Weight, kg(SD);
Head circumference, cm(SD);
Age at folow-up/measurements, years;
Neurodevelopment;
Language/speech delay;
First words, months;
First steps, months;
IQ profile;
nan;
nan;
Behavior problems;
Psychosis / Schizophrenia;
Use of psychiatric drugs;
Other_neurodev;
Neurological;
Seizures / Epilepsy;
Dystonia, if present - type and age of onset;
Other neurological/movement issues;
Brain MRI findings;
Musculoskeletal/extremities;
Vertebral abnormalities (Scoliosis, kyphosis etc).;
Hand /foot/ finger abnormalities;
Other_musculoskel;
Dysmorphism;
Dysmorphic features;
Lip/palate cleft;
Eyes/visual problems;
Hypermetropia/myopia;
Other_eye;
Ear/ hearing problems;
Hearing;
Other_ear;
Cardiovascular;
Congenital heart disease;
Other_cv;
Gastrointestinal;
Neonatal feeding difficulties;
Yes;
Other_gi;
Skin hyperlaxity;
Genitourinary abnormalities;
Other medication received;
Other;
nan;
nan;
nan;
patient_id
\n", - " | terms | \n", - "
---|---|
0 | \n", - "HP:0000718 (Aggressive behavior/observed) | \n", - "
1 | \n", - "HP:0000708 (Atypical behavior/excluded) | \n", - "
2 | \n", - "n/a | \n", - "
3 | \n", - "HP:0000708 (Atypical behavior/observed) | \n", - "
4 | \n", - "n/a | \n", - "
... | \n", - "... | \n", - "
68 | \n", - "HP:0000708 (Atypical behavior/excluded) | \n", - "
69 | \n", - "n/a | \n", - "
70 | \n", - "n/a | \n", - "
71 | \n", - "n/a | \n", - "
72 | \n", - "n/a | \n", - "
73 rows × 1 columns
\n", - "\n", - " | original column contents | \n", - "sex | \n", - "
---|---|---|
0 | \n", - "F | \n", - "FEMALE | \n", - "
1 | \n", - "F | \n", - "FEMALE | \n", - "
2 | \n", - "M | \n", - "MALE | \n", - "
3 | \n", - "M | \n", - "MALE | \n", - "
4 | \n", - "M | \n", - "MALE | \n", - "
... | \n", - "... | \n", - "... | \n", - "
68 | \n", - "M | \n", - "MALE | \n", - "
69 | \n", - "M | \n", - "MALE | \n", - "
70 | \n", - "M | \n", - "MALE | \n", - "
71 | \n", - "M | \n", - "MALE | \n", - "
72 | \n", - "M | \n", - "MALE | \n", - "
73 rows × 2 columns
\n", - "Errors found with 53 of 73 phenopackets.
\n", + "Level | Error category | Count |
---|---|---|
ERROR | CONFLICT | 6 |
WARNING | REDUNDANT | 33 |
INFORMATION | NOT_MEASURED | 66 |
A total of 105 issues were fixed and no individual was removed from the cohort.
" + ], + "text/plain": [ + "Errors found with 1 of 73 phenopackets.
\n", + "Level | Error category | Count |
---|---|---|
WARNING | REDUNDANT | 1 |
A total of 1 issues were fixed and no individual was removed from the cohort.
" + ], + "text/plain": [ + "No errors found for the cohort with 73 individuals
" + ], + "text/plain": [ + "Individual | Disease | Genotype | Phenotypic features |
---|---|---|---|
Individual 1 (FEMALE; P16Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.1018del (heterozygous) | Motor delay (HP:0001270); Specific learning disability (HP:0001328); Autistic behavior (HP:0000729); Recurrent otitis media (HP:0000403); Aggressive behavior (HP:0000718); Large for gestational age (HP:0001520); Obesity (HP:0001513); Delayed speech and language development (HP:0000750); Brachydactyly (HP:0001156); Clinodactyly (HP:0030084); Broad foot (HP:0001769); Depressed nasal bridge (HP:0005280); Epicanthus (HP:0000286); Broad chin (HP:0011822); Anteverted nares (HP:0000463); Thin vermilion border (HP:0000233); Coarse facial features (HP:0000280); Square face (HP:0000321); Supernumerary nipple (HP:0002558); Mild hypermetropia (HP:0031728); Feeding difficulties (HP:0011968); Hypernasal speech (HP:0001611); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Constipation (HP:0002019); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175) |
Individual 2 (FEMALE; P10Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.1085_1088del (heterozygous) | Motor delay (HP:0001270); Intellectual disability, mild (HP:0001256); Joint hypermobility (HP:0001382); Delayed speech and language development (HP:0000750); Global developmental delay (HP:0001263); Intention tremor (HP:0002080); Clubbing of fingers (HP:0100759); Hip dysplasia (HP:0001385); Prominent forehead (HP:0011220); Mandibular prognathia (HP:0000303); Hypermetropia (HP:0000540); Feeding difficulties (HP:0011968); Cafe-au-lait spot (HP:0000957); excluded: Autistic behavior (HP:0000729); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Hypermetropia (HP:0000540); excluded: Increased body weight (HP:0004324) |
Individual 3 (MALE; P9Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.654_655del (heterozygous) | Motor delay (HP:0001270); Intellectual disability, moderate (HP:0002342); Autistic behavior (HP:0000729); Sleep abnormality (HP:0002360); Joint hypermobility (HP:0001382); Recurrent otitis media (HP:0000403); Constipation (HP:0002019); Irritability (HP:0000737); Anxiety (HP:0000739); Large for gestational age (HP:0001520); Obesity (HP:0001513); Macrocephaly (HP:0000256); Delayed speech and language development (HP:0000750); Clinodactyly (HP:0030084); Broad foot (HP:0001769); Square face (HP:0000321); Depressed nasal bridge (HP:0005280); Epicanthus (HP:0000286); Protruding ear (HP:0000411); Feeding difficulties (HP:0011968); Cafe-au-lait spot (HP:0000957); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Irritability (HP:0000737); excluded: Anxiety (HP:0000739); excluded: Obstipation (HP:0034782); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539) |
Individual 5 (MALE; P25Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.1439dup (heterozygous) | Motor delay (HP:0001270); Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Recurrent otitis media (HP:0000403); Delayed speech and language development (HP:0000750); Seizure (HP:0001250); Hypertonia (HP:0001276); Involuntary movements (HP:0004305); Pes planus (HP:0001763); Broad finger (HP:0001500); Deeply set eye (HP:0000490); Synophrys (HP:0000664); Thick lower lip vermilion (HP:0000179); Allergy (HP:0012393); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Constipation (HP:0002019); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539); excluded: Feeding difficulties (HP:0011968) |
Individual 6 (MALE; P13Y2M) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.2598del (heterozygous) | Motor delay (HP:0001270); Intellectual disability, mild (HP:0001256); Attention deficit hyperactivity disorder (HP:0007018); Maternal diabetes (HP:0009800); Delayed speech and language development (HP:0000750); Relative macrocephaly (HP:0004482); Synophrys (HP:0000664); Hypermetropia (HP:0000540); Phimosis (HP:0001741); excluded: Autistic behavior (HP:0000729); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Hypermetropia (HP:0000540); excluded: Feeding difficulties (HP:0011968) |
Individual 7 (FEMALE; P9Y6M) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4500C>A (heterozygous) | Specific learning disability (HP:0001328); Sleep abnormality (HP:0002360); Aggressive behavior (HP:0000718); Premature rupture of membranes (HP:0001788); Delayed speech and language development (HP:0000750); Seizure (HP:0001250); Tics (HP:0100033); Short nose (HP:0003196); Short philtrum (HP:0000322); Thick vermilion border (HP:0012471); Preauricular pit (HP:0004467); Feeding difficulties (HP:0011968); Supernumerary maxillary incisor (HP:0006332); excluded: Motor delay (HP:0001270); excluded: Autistic behavior (HP:0000729); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539) |
Individual 8 (MALE; P10Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.403C>T (heterozygous) | Motor delay (HP:0001270); Intellectual disability, mild (HP:0001256); Autistic behavior (HP:0000729); Sleep abnormality (HP:0002360); Hypotonia (HP:0001252); Joint hypermobility (HP:0001382); Attention deficit hyperactivity disorder (HP:0007018); Breech presentation (HP:0001623); Large for gestational age (HP:0001520); Tall stature (HP:0000098); Delayed speech and language development (HP:0000750); Cerebellar cortical atrophy (HP:0008278); Kyphosis (HP:0002808); Clinodactyly (HP:0030084); Hypotelorism (HP:0000601); Short philtrum (HP:0000322); Prominent nasal bridge (HP:0000426); Brachycephaly (HP:0000248); Congenital hip dislocation (HP:0001374); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Kyphosis (HP:0002808); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539); excluded: Feeding difficulties (HP:0011968) |
Individual 9 (MALE; P6Y6M) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4737+1G>A (heterozygous) | Motor delay (HP:0001270); Hypotonia (HP:0001252); Joint hypermobility (HP:0001382); Ventouse delivery (HP:0011412); Delayed speech and language development (HP:0000750); Global developmental delay (HP:0001263); Preauricular skin tag (HP:0000384); Abnormality of refraction (HP:0000539); excluded: Sleep abnormality (HP:0002360); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Feeding difficulties (HP:0011968) |
Individual 11 (FEMALE; P19Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.3288_3291del (heterozygous) | Motor delay (HP:0001270); Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Hypotonia (HP:0001252); Delayed speech and language development (HP:0000750); Psychosis (HP:0000709); Ataxia (HP:0001251); Hearing impairment (HP:0000365); Enlarged vestibular aqueduct (HP:0011387); Recurrent skin infections (HP:0001581); excluded: Sleep abnormality (HP:0002360); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539); excluded: Hearing impairment (HP:0000365); excluded: Feeding difficulties (HP:0011968) |
Individual 12 (MALE; P17Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.3288_3291del (heterozygous) | Motor delay (HP:0001270); Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Hypotonia (HP:0001252); Macrocephaly (HP:0000256); Delayed speech and language development (HP:0000750); Psychosis (HP:0000709); Dystonia (HP:0001332); Vomiting (HP:0002013); Hypercalcemia (HP:0003072); excluded: Sleep abnormality (HP:0002360); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Seizure (HP:0001250); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539); excluded: Feeding difficulties (HP:0011968) |
Individual 13 (FEMALE; P6Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.403C>T (heterozygous) | Motor delay (HP:0001270); Intellectual disability, mild (HP:0001256); Obstructive sleep apnea (HP:0002870); Hypotonia (HP:0001252); Severe temper tantrums (HP:0025162); Delayed speech and language development (HP:0000750); Neurogenic bladder (HP:0000011); Tethered cord (HP:0002144); Macrocephaly (HP:0000256); Prominent forehead (HP:0011220); Wide mouth (HP:0000154); Joint hypermobility (HP:0001382); Feeding difficulties (HP:0011968); Failure to thrive (HP:0001508); Livedo reticularis (HP:0033505); excluded: Autistic behavior (HP:0000729); excluded: Obstructive sleep apnea (HP:0002870); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539) |
Individual 15 (MALE; P5Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.138-1G>A (heterozygous) | Motor delay (HP:0001270); Intellectual disability, moderate (HP:0002342); Autistic behavior (HP:0000729); Sleep apnea (HP:0010535); Hypotonia (HP:0001252); Joint hypermobility (HP:0001382); Exotropia (HP:0000577); Constipation (HP:0002019); Attention deficit hyperactivity disorder (HP:0007018); Aggressive behavior (HP:0000718); Small for gestational age (HP:0001518); Delayed speech and language development (HP:0000750); Generalized non-motor (absence) seizure (HP:0002121); Bilateral tonic-clonic seizure (HP:0002069); Hypertelorism (HP:0000316); Mandibular prognathia (HP:0000303); Hypodontia (HP:0000668); Microdontia (HP:0000691); Cryptorchidism (HP:0000028); Patent ductus arteriosus (HP:0001643); Feeding difficulties (HP:0011968); Pneumonia (HP:0002090); excluded: Sleep apnea (HP:0010535); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Exotropia (HP:0000577); excluded: Recurrent otitis media (HP:0000403); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Generalized non-motor (absence) seizure (HP:0002121); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539); excluded: Feeding difficulties (HP:0011968) |
Individual 16 (MALE; P12Y 4M) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.523C>T (heterozygous) | Motor delay (HP:0001270); Specific learning disability (HP:0001328); Autistic behavior (HP:0000729); Sleep abnormality (HP:0002360); Impulsivity (HP:0100710); Delayed speech and language development (HP:0000750); Psychosis (HP:0000709); Tics (HP:0100033); Rhinitis (HP:0012384); Polyphagia (HP:0002591); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Impulsivity (HP:0100710); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539); excluded: Feeding difficulties (HP:0011968) |
Individual 17 (published as Individual 1 in Bramswig et al., 2017) (MALE; P14Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4733del (heterozygous) | Motor delay (HP:0001270); Intellectual disability, severe (HP:0010864); Hypotonia (HP:0001252); Delayed speech and language development (HP:0000750); Seizure (HP:0001250); Cerebral atrophy (HP:0002059); Agenesis of corpus callosum (HP:0001274); Scoliosis (HP:0002650); Coarse facial features (HP:0000280); Hypertelorism (HP:0000316); Depressed nasal bridge (HP:0005280); Short nose (HP:0003196); Anteverted nares (HP:0000463); Low-set ears (HP:0000369); Everted lower lip vermilion (HP:0000232); Secundum atrial septal defect (HP:0001684); Feeding difficulties (HP:0011968); Unilateral renal agenesis (HP:0000122); excluded: Autistic behavior (HP:0000729); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539) |
Individual 18 (MALE; P19Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.1085_1088del (heterozygous) | Specific learning disability (HP:0001328); Autistic behavior (HP:0000729); Knee joint hypermobility (HP:0045086); Constipation (HP:0002019); Anxiety (HP:0000739); Aggressive behavior (HP:0000718); Large for gestational age (HP:0001520); Developmental regression (HP:0002376); Prominent interphalangeal joints (HP:0006237); Macrocephaly (HP:0000256); Thin upper lip vermilion (HP:0000219); Myopia (HP:0000545); Asthma (HP:0002099); Pneumonia (HP:0002090); Inguinal hernia (HP:0000023); excluded: Motor delay (HP:0001270); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Anxiety (HP:0000739); excluded: Aggressive behavior (HP:0000718); excluded: Delayed speech and language development (HP:0000750); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Myopia (HP:0000545) |
Individual 19 (MALE; P6Y6M) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.445C>T (heterozygous) | Motor delay (HP:0001270); Specific learning disability (HP:0001328); Autistic behavior (HP:0000729); Fetal distress (HP:0025116); Delayed speech and language development (HP:0000750); Global developmental delay (HP:0001263); Ptosis (HP:0000508); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539); excluded: Feeding difficulties (HP:0011968) |
Individual 20 (FEMALE; P2Y8M) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.3911_3912del (heterozygous) | Motor delay (HP:0001270); Hypotonia (HP:0001252); Ventouse delivery (HP:0011412); Delayed speech and language development (HP:0000750); Coarse facial features (HP:0000280); Prominent forehead (HP:0011220); Depressed nasal bridge (HP:0005280); Plagiocephaly (HP:0001357); excluded: Autistic behavior (HP:0000729); excluded: Sleep abnormality (HP:0002360); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Feeding difficulties (HP:0011968) |
Individual 21 (MALE; P10Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.2572C>T (heterozygous) | Motor delay (HP:0001270); Intellectual disability, severe (HP:0010864); Autistic behavior (HP:0000729); Sleep abnormality (HP:0002360); Hypotonia (HP:0001252); Attention deficit hyperactivity disorder (HP:0007018); Large for gestational age (HP:0001520); Delayed speech and language development (HP:0000750); Broad fingertip (HP:0011300); External tibial torsion (HP:0034373); Infra-orbital crease (HP:0100876); Deep philtrum (HP:0002002); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539); excluded: Feeding difficulties (HP:0011968) |
Individual 22 (MALE; P10Y5M) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.2699del (heterozygous) | Motor delay (HP:0001270); Intellectual disability, borderline (HP:0006889); Tip-toe gait (HP:0030051); Toe syndactyly (HP:0001770); Intrauterine growth retardation (HP:0001511); Delayed speech and language development (HP:0000750); Bruxism (HP:0003763); Dystonia (HP:0001332); Dysarthria (HP:0001260); Fused cervical vertebrae (HP:0002949); Low anterior hairline (HP:0000294); Depressed nasal bridge (HP:0005280); Anteverted nares (HP:0000463); Smooth philtrum (HP:0000319); Thin upper lip vermilion (HP:0000219); Broad face (HP:0000283); Full cheeks (HP:0000293); Hypermetropia (HP:0000540); Astigmatism (HP:0000483); Cafe-au-lait spot (HP:0000957); excluded: Autistic behavior (HP:0000729); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Tip-toe gait (HP:0030051); excluded: Toe syndactyly (HP:0001770); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Hypermetropia (HP:0000540); excluded: Feeding difficulties (HP:0011968) |
Individual 23 (MALE; P4Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.1537dup (heterozygous) | Motor delay (HP:0001270); Hypotonia (HP:0001252); Agitation (HP:0000713); Large for gestational age (HP:0001520); Delayed speech and language development (HP:0000750); Prominent nose (HP:0000448); Feeding difficulties (HP:0011968); Duplication of renal pelvis (HP:0005580); excluded: Autistic behavior (HP:0000729); excluded: Sleep abnormality (HP:0002360); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Constipation (HP:0002019); excluded: Agitation (HP:0000713); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175) |
Individual 24 (FEMALE; P8Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.3674-2A>G (heterozygous) | Motor delay (HP:0001270); Hypotonia (HP:0001252); Constipation (HP:0002019); Aggressive behavior (HP:0000718); Tethered cord (HP:0002144); Scoliosis (HP:0002650); Macrocephaly (HP:0000256); Hypertelorism (HP:0000316); Prominent eyelashes (HP:0011231); Overfolded helix (HP:0000396); Diastema (HP:0000699); Mandibular prognathia (HP:0000303); Pulmonic stenosis (HP:0001642); Feeding difficulties (HP:0011968); Eosinophilic infiltration of the esophagus (HP:0410151); excluded: Sleep abnormality (HP:0002360); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Aggressive behavior (HP:0000718); excluded: Delayed speech and language development (HP:0000750); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175) |
Individual 25 (FEMALE; P4Y10M) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.654_655del (heterozygous) | Motor delay (HP:0001270); Anxiety (HP:0000739); Maternal diabetes (HP:0009800); Delayed speech and language development (HP:0000750); Drooling (HP:0002307); Deeply set eye (HP:0000490); Strabismus (HP:0000486); Full cheeks (HP:0000293); Depressed nasal bridge (HP:0005280); Anteverted nares (HP:0000463); Square face (HP:0000321); Synophrys (HP:0000664); Hypermetropia (HP:0000540); Feeding difficulties (HP:0011968); excluded: Autistic behavior (HP:0000729); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Recurrent otitis media (HP:0000403); excluded: Anxiety (HP:0000739); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Hypermetropia (HP:0000540) |
Individual 26 (MALE; P26Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.3300del (heterozygous) | Motor delay (HP:0001270); Sleep abnormality (HP:0002360); Joint hypermobility (HP:0001382); Depression (HP:0000716); Attention deficit hyperactivity disorder (HP:0007018); Hydrocephalus (HP:0000238); Delayed speech and language development (HP:0000750); Psychosis (HP:0000709); Platybasia (HP:0002691); Small foramen magnum (HP:0002677); Pes planus (HP:0001763); Myopia (HP:0000545); Nystagmus (HP:0000639); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Depression (HP:0000716); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Anxiety (HP:0000739); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Cleft palate (HP:0000175); excluded: Astigmatism (HP:0000483); excluded: Myopia (HP:0000545); excluded: Feeding difficulties (HP:0011968) |
Individual 27 (MALE; P7Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.3038del (heterozygous) | Motor delay (HP:0001270); Sleep abnormality (HP:0002360); Hypotonia (HP:0001252); Tip-toe gait (HP:0030051); Recurrent otitis media (HP:0000403); Shoulder dystocia (HP:0011413); Delayed speech and language development (HP:0000750); Fatigue (HP:0012378); Brachydactyly (HP:0001156); Long face (HP:0000276); Depressed nasal bridge (HP:0005280); Anteverted nares (HP:0000463); Downslanted palpebral fissures (HP:0000494); Long philtrum (HP:0000343); Feeding difficulties (HP:0011968); Diarrhea (HP:0002014); excluded: Autistic behavior (HP:0000729); excluded: Tip-toe gait (HP:0030051); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539) |
Individual 28 (MALE; P10Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.3944+1G>A (heterozygous) | Motor delay (HP:0001270); Intellectual disability, mild (HP:0001256); Autistic behavior (HP:0000729); Hypotonia (HP:0001252); Joint hypermobility (HP:0001382); Aggressive behavior (HP:0000718); Delayed speech and language development (HP:0000750); Fatigue (HP:0012378); Hypermetropia (HP:0000540); excluded: Sleep abnormality (HP:0002360); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Hypermetropia (HP:0000540); excluded: Feeding difficulties (HP:0011968) |
Individual 29 (FEMALE; P13Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.1260_1270del (heterozygous) | Motor delay (HP:0001270); Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Sleep abnormality (HP:0002360); Hypotonia (HP:0001252); Maternal diabetes (HP:0009800); Delayed speech and language development (HP:0000750); Focal impaired awareness seizure (HP:0002384); Scoliosis (HP:0002650); High forehead (HP:0000348); Horizontal eyebrow (HP:0011228); Prominent nasal bridge (HP:0000426); Wide mouth (HP:0000154); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Focal impaired awareness seizure (HP:0002384); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Feeding difficulties (HP:0011968) |
Individual 31 (FEMALE; P12Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.496C>T (heterozygous) | Motor delay (HP:0001270); Intellectual disability, mild (HP:0001256); Hypotonia (HP:0001252); Obesity (HP:0001513); Delayed speech and language development (HP:0000750); Small hand (HP:0200055); Clinodactyly (HP:0030084); Prominent nasal bridge (HP:0000426); Ptosis (HP:0000508); Prominent forehead (HP:0011220); Mandibular prognathia (HP:0000303); Myopia (HP:0000545); Esotropia (HP:0000565); Amblyopia (HP:0000646); Feeding difficulties (HP:0011968); Adrenal insufficiency (HP:0000846); excluded: Autistic behavior (HP:0000729); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Myopia (HP:0000545); excluded: Esotropia (HP:0000565); excluded: Lethargy (HP:0001254) |
Individual 32 (MALE; P14Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.419dup (heterozygous) | Motor delay (HP:0001270); Autistic behavior (HP:0000729); Hypotonia (HP:0001252); Hyperextensible hand joints (HP:0005639); Constipation (HP:0002019); Cryptorchidism (HP:0000028); Aggressive behavior (HP:0000718); Anxiety (HP:0000739); Hypertension (HP:0000822); Delayed speech and language development (HP:0000750); Enuresis (HP:0000805); Brachydactyly (HP:0001156); Macrocephaly (HP:0000256); Anteverted nares (HP:0000463); Bicuspid aortic valve (HP:0001647); Increased body weight (HP:0004324); Premature adrenarche (HP:0012412); excluded: Sleep abnormality (HP:0002360); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Anxiety (HP:0000739); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539); excluded: Feeding difficulties (HP:0011968) |
Individual 33 (MALE; P7Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.2985_2988delinsGGGACAGTGCC (heterozygous) | Motor delay (HP:0001270); Intellectual disability, mild (HP:0001256); Autistic behavior (HP:0000729); Hypotonia (HP:0001252); Joint hypermobility (HP:0001382); Abnormal repetitive mannerisms (HP:0000733); Large for gestational age (HP:0001520); Obesity (HP:0001513); Delayed speech and language development (HP:0000750); Poor coordination (HP:0002370); Hyperlordosis (HP:0003307); Broad foot (HP:0001769); High anterior hairline (HP:0009890); Prominent forehead (HP:0011220); Hypertelorism (HP:0000316); Wide mouth (HP:0000154); Protruding ear (HP:0000411); Hypermetropia (HP:0000540); Astigmatism (HP:0000483); excluded: Sleep abnormality (HP:0002360); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Abnormal repetitive mannerisms (HP:0000733); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Hyperlordosis (HP:0003307); excluded: Cleft palate (HP:0000175); excluded: Hypermetropia (HP:0000540); excluded: Feeding difficulties (HP:0011968) |
Individual 37 (MALE; P4Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.2690_2703del (heterozygous) | Motor delay (HP:0001270); Intellectual disability (HP:0001249); Hypotonia (HP:0001252); Aggressive behavior (HP:0000718); Delayed speech and language development (HP:0000750); Myoclonic seizure (HP:0032794); Prominent forehead (HP:0011220); Ventricular septal defect (HP:0001629); Subvalvular aortic stenosis (HP:0001682); Interrupted aortic arch (HP:0011611); Atrial septal defect (HP:0001631); excluded: Autistic behavior (HP:0000729); excluded: Sleep abnormality (HP:0002360); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Psychosis (HP:0000709); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539); excluded: Feeding difficulties (HP:0011968) |
Individual 39 (MALE; P4Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.1229_1233dup (heterozygous) | Motor delay (HP:0001270); Intellectual disability, mild (HP:0001256); Constipation (HP:0002019); Delayed speech and language development (HP:0000750); excluded: Autistic behavior (HP:0000729); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539); excluded: Feeding difficulties (HP:0011968) |
Individual 40 (DDD_304502) (MALE; P3Y10M) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.2923C>T (heterozygous) | Motor delay (HP:0001270); Intellectual disability, mild (HP:0001256); Large for gestational age (HP:0001520); Obesity (HP:0001513); Delayed speech and language development (HP:0000750); Moderate global developmental delay (HP:0011343); Prominent fingertip pads (HP:0001212); Down-sloping shoulders (HP:0200021); Tall stature (HP:0000098); Talipes (HP:0001883); Downturned corners of mouth (HP:0002714); Cleft palate (HP:0000175); Feeding difficulties (HP:0011968); excluded: Autistic behavior (HP:0000729); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539) |
Individual 41 (DDD_274859) (FEMALE; P6Y5M) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.3535dup (heterozygous) | Motor delay (HP:0001270); Moderate intrauterine growth retardation (HP:0011408); Small for gestational age (HP:0001518); Delayed speech and language development (HP:0000750); Moderate global developmental delay (HP:0011343); Short attention span (HP:0000736); Proportionate tall stature (HP:0011407); Feeding difficulties (HP:0011968); excluded: Autistic behavior (HP:0000729); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Short attention span (HP:0000736); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539) |
Individual 42 (DDD_292095) (MALE; P4Y6M) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.3564_3567del (heterozygous) | Motor delay (HP:0001270); Autistic behavior (HP:0000729); Delayed speech and language development (HP:0000750); Developmental regression (HP:0002376); Feeding difficulties (HP:0011968); Cafe-au-lait spot (HP:0000957); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539) |
Individual 45 (DDD_111002863) (MALE; P3Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.685C>T (heterozygous) | Motor delay (HP:0001270); Intellectual disability (HP:0001249); Atypical behavior (HP:0000708); Polyhydramnios (HP:0001561); Macrocephaly (HP:0000256); Delayed speech and language development (HP:0000750); Pes planus (HP:0001763); Freckling (HP:0001480); Posteriorly rotated ears (HP:0000358); Deeply set eye (HP:0000490); Frontal bossing (HP:0002007); excluded: Autistic behavior (HP:0000729); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539); excluded: Feeding difficulties (HP:0011968) |
Individual 46 (DDD_118000039) (MALE; P4Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.2923C>T (heterozygous) | Motor delay (HP:0001270); Intellectual disability (HP:0001249); Hypotonia (HP:0001252); Delayed speech and language development (HP:0000750); Unsteady gait (HP:0002317); Pes planus (HP:0001763); Wide mouth (HP:0000154); Macroglossia (HP:0000158); Short nose (HP:0003196); Uplifted earlobe (HP:0009909); Ptosis (HP:0000508); excluded: Autistic behavior (HP:0000729); excluded: Sleep abnormality (HP:0002360); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Aggressive behavior (HP:0000718); excluded: Seizure (HP:0001250); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539) |
Individual 47 (DDD_303829) (FEMALE; P8Y8M) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.1416_1417del (heterozygous) | Motor delay (HP:0001270); Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Hypotonia (HP:0001252); Joint hypermobility (HP:0001382); Ventouse delivery (HP:0011412); Macrocephaly (HP:0000256); Delayed speech and language development (HP:0000750); Pes planus (HP:0001763); Macrotia (HP:0000400); Deeply set eye (HP:0000490); High palate (HP:0000218); Widely spaced teeth (HP:0000687); excluded: Autistic behavior (HP:0000729); excluded: Hyperorality (HP:0000710); excluded: Sleep abnormality (HP:0002360); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539); excluded: Feeding difficulties (HP:0011968) |
Individual 48 (TAS_F3039Y) (MALE; P23Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4795del (heterozygous) | Motor delay (HP:0001270); Specific learning disability (HP:0001328); Autistic behavior (HP:0000729); Sleep abnormality (HP:0002360); Aggressive behavior (HP:0000718); Attention deficit hyperactivity disorder (HP:0007018); Delayed speech and language development (HP:0000750); Abnormal social behavior (HP:0012433); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Abnormality of refraction (HP:0000539); excluded: Feeding difficulties (HP:0011968) |
Individual 51 (ASC_80001103038) (MALE; P8 Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.2134C>T (heterozygous) | Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Delayed speech and language development (HP:0000750); Seizure (HP:0001250); excluded: Motor delay (HP:0001270); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Psychosis (HP:0000709); excluded: Dystonia (HP:0001332) |
Individual 52 (SSC_12683.p1) (MALE; n/a) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.578del (heterozygous) | Autistic behavior (HP:0000729) |
Individual 53 (SSC_11329.p1) (MALE; n/a) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.138-2A>G (heterozygous) | Autistic behavior (HP:0000729) |
Individual 55 (SSC_13446.p1) (MALE; n/a) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4468+5G>C (heterozygous) | Autistic behavior (HP:0000729) |
Individual 56 (ASP009) (FEMALE; P25Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.2125G>T (heterozygous) | Autistic behavior (HP:0000729); Strabismus (HP:0000486); Attention deficit hyperactivity disorder (HP:0007018); Delayed speech and language development (HP:0000750); Depression (HP:0000716); Seizure (HP:0001250); excluded: Motor delay (HP:0001270); excluded: Psychosis (HP:0000709) |
Individual 57 (PCGC_1-03321) (MALE; P4Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4708G>T (heterozygous) | Strabismus (HP:0000486); Small for gestational age (HP:0001518); Delayed speech and language development (HP:0000750); Periventricular leukomalacia (HP:0006970); Sacral dimple (HP:0000960); Male urethral meatus stenosis (HP:0032077); excluded: Autistic behavior (HP:0000729); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175) |
Individual 60 (MSSNG_AU4427301) (MALE; n/a) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.343C>T (heterozygous) | Motor delay (HP:0001270); Autistic behavior (HP:0000729); Delayed speech and language development (HP:0000750); Poor coordination (HP:0002370); excluded: Aggressive behavior (HP:0000718) |
Individual 61 (MSSNG_MT_48.3) (FEMALE; n/a) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.403C>T (heterozygous) | Autistic behavior (HP:0000729) |
Individual 62 (MSSNG_AU2168301) (MALE; n/a) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.2012_2013del (heterozygous) | Motor delay (HP:0001270); Autistic behavior (HP:0000729); Delayed speech and language development (HP:0000750); excluded: Aggressive behavior (HP:0000718); excluded: Scoliosis (HP:0002650) |
Individual 63 (MSSNG_2-1764-003) (MALE; n/a) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4165+2T>A (heterozygous) | Autistic behavior (HP:0000729); Hypotonia (HP:0001252); Constipation (HP:0002019); Tics (HP:0100033) |
Individual 65 (FEMALE; P11Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.2970dup (heterozygous) | Motor delay (HP:0001270); Intellectual disability, mild (HP:0001256); Sleep abnormality (HP:0002360); Hypotonia (HP:0001252); Macrocephaly (HP:0000256); Delayed speech and language development (HP:0000750); Dilation of Virchow-Robin spaces (HP:0012520); High forehead (HP:0000348); Horizontal eyebrow (HP:0011228); Deeply set eye (HP:0000490); Dimple chin (HP:0010751); Prominent nasal bridge (HP:0000426); Hypermetropia (HP:0000540); Horizontal nystagmus (HP:0000666); excluded: Autistic behavior (HP:0000729); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Hypermetropia (HP:0000540); excluded: Astigmatism (HP:0000483); excluded: Feeding difficulties (HP:0011968) |
Individual 67 (MALE; P5Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.1769del (heterozygous) | Motor delay (HP:0001270); Hypotonia (HP:0001252); Joint hypermobility (HP:0001382); Macrocephaly (HP:0000256); Delayed speech and language development (HP:0000750); Recurrent hand flapping (HP:0100023); Hydrocephalus (HP:0000238); Thoracic kyphosis (HP:0002942); Pes planus (HP:0001763); High forehead (HP:0000348); Downslanted palpebral fissures (HP:0000494); Deeply set eye (HP:0000490); Dimple chin (HP:0010751); Downturned corners of mouth (HP:0002714); Large earlobe (HP:0009748); Abnormality of refraction (HP:0000539); Inguinal freckling (HP:0030052); excluded: Autistic behavior (HP:0000729); excluded: Sleep abnormality (HP:0002360); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Thoracic kyphosis (HP:0002942); excluded: Cleft palate (HP:0000175); excluded: Feeding difficulties (HP:0011968) |
Individual 68 (FEMALE; P35Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.1769del (heterozygous) | Motor delay (HP:0001270); Joint hypermobility (HP:0001382); Pes planus (HP:0001763); Mild myopia (HP:0025573); Cafe-au-lait spot (HP:0000957); excluded: Autistic behavior (HP:0000729); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Delayed speech and language development (HP:0000750); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Feeding difficulties (HP:0011968) |
Individual 70 (MALE; P8Y11M) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.1053_1056del (heterozygous) | Sleep abnormality (HP:0002360); Joint hypermobility (HP:0001382); Recurrent otitis media (HP:0000403); Hyperactivity (HP:0000752); Delayed speech and language development (HP:0000750); Midface retrusion (HP:0011800); Short nose (HP:0003196); Short philtrum (HP:0000322); Wide mouth (HP:0000154); Eclabion (HP:0012472); Anteverted nares (HP:0000463); Hypermetropia (HP:0000540); excluded: Motor delay (HP:0001270); excluded: Autistic behavior (HP:0000729); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Constipation (HP:0002019); excluded: Hyperactivity (HP:0000752); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Cleft palate (HP:0000175); excluded: Hypermetropia (HP:0000540); excluded: Feeding difficulties (HP:0011968) |
Individual 71 (MALE; P7Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.2448C>G (heterozygous) | Motor delay (HP:0001270); Intellectual disability, mild (HP:0001256); Autistic behavior (HP:0000729); Sleep abnormality (HP:0002360); Hypotonia (HP:0001252); Joint hypermobility (HP:0001382); Macrocephaly (HP:0000256); Delayed speech and language development (HP:0000750); Poor gross motor coordination (HP:0007015); Prominent forehead (HP:0011220); Sparse eyebrow (HP:0045075); Uplifted earlobe (HP:0009909); Protruding ear (HP:0000411); Smooth philtrum (HP:0000319); Astigmatism (HP:0000483); Feeding difficulties (HP:0011968); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Astigmatism (HP:0000483) |
Individual 72 (MALE; P7Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4020_4021delinsAT (heterozygous) | Motor delay (HP:0001270); Strabismus (HP:0000486); Attention deficit hyperactivity disorder (HP:0007018); Small for gestational age (HP:0001518); Delayed speech and language development (HP:0000750); Prominent forehead (HP:0011220); Short nose (HP:0003196); Protruding ear (HP:0000411); excluded: Autistic behavior (HP:0000729); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Pectus excavatum (HP:0000767); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175) |
Individual 73 (MALE; P10Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.1416_1417del (heterozygous) | Motor delay (HP:0001270); Intellectual disability, mild (HP:0001256); Autistic behavior (HP:0000729); Hypotonia (HP:0001252); Joint hypermobility (HP:0001382); Attention deficit hyperactivity disorder (HP:0007018); Delayed speech and language development (HP:0000750); Single transverse palmar crease (HP:0000954); Hip dysplasia (HP:0001385); Hypertelorism (HP:0000316); Microcephaly (HP:0000252); Short chin (HP:0000331); Protruding ear (HP:0000411); Mild hypermetropia (HP:0031728); excluded: Pectus excavatum (HP:0000767); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Cleft palate (HP:0000175) |
Individual 74 (MALE; P49Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.1416_1417del (heterozygous) | Specific learning disability (HP:0001328); excluded: Pectus excavatum (HP:0000767) |
Individual 75 (MALE; P9Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.2865del (heterozygous) | Motor delay (HP:0001270); Hypotonia (HP:0001252); Impulsivity (HP:0100710); Delayed speech and language development (HP:0000750); Kyphosis (HP:0002808); Pes planus (HP:0001763); Prominent forehead (HP:0011220); Midface retrusion (HP:0011800); Macrocephaly (HP:0000256); excluded: Sleep abnormality (HP:0002360); excluded: Pectus excavatum (HP:0000767); excluded: Impulsivity (HP:0100710); excluded: Kyphosis (HP:0002808); excluded: Cleft palate (HP:0000175) |
Individual 76 (FEMALE; P14Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4431G>A (heterozygous) | Motor delay (HP:0001270); Central sleep apnea (HP:0010536); Hypotonia (HP:0001252); Joint hypermobility (HP:0001382); Delayed speech and language development (HP:0000750); Genu valgum (HP:0002857); Short toe (HP:0001831); Pes planus (HP:0001763); Patellar subluxation (HP:0010499); Wide nose (HP:0000445); Full cheeks (HP:0000293); Epicanthus (HP:0000286); Astigmatism (HP:0000483); Feeding difficulties (HP:0011968); Alopecia (HP:0001596); excluded: Autistic behavior (HP:0000729); excluded: Central sleep apnea (HP:0010536); excluded: Syndactyly (HP:0001159); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Cleft palate (HP:0000175) |
Individual 77 (MALE; P19Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.1483C>T (heterozygous) | Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Sleep abnormality (HP:0002360); Strabismus (HP:0000486); Decreased fetal movement (HP:0001558); Macrocephaly (HP:0000256); Delayed speech and language development (HP:0000750); Seizure (HP:0001250); Pes planus (HP:0001763); Prominent forehead (HP:0011220); Synophrys (HP:0000664); Wide nose (HP:0000445); Wide mouth (HP:0000154); Thick vermilion border (HP:0012471); Hypermetropia (HP:0000540); excluded: Motor delay (HP:0001270); excluded: Hypotonia (HP:0001252); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Focal-onset seizure (HP:0007359); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Hypermetropia (HP:0000540); excluded: Feeding difficulties (HP:0011968) |
Individual 82 (FEMALE; P1.5Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.1085_1088del (heterozygous) | Motor delay (HP:0001270); Sleep abnormality (HP:0002360); Hypotonia (HP:0001252); Joint hypermobility (HP:0001382); Constipation (HP:0002019); Decreased fetal movement (HP:0001558); Delayed speech and language development (HP:0000750); Sensory seeking (HP:4000079); Seizure (HP:0001250); High forehead (HP:0000348); Short nose (HP:0003196); Full cheeks (HP:0000293); Patent ductus arteriosus (HP:0001643); Feeding difficulties (HP:0011968); Facial telangiectasia (HP:0007380); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539) |
Individual 83 (MALE; P8Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.3046dup (heterozygous) | Motor delay (HP:0001270); Intellectual disability (HP:0001249); Autistic behavior (HP:0000729); Sleep abnormality (HP:0002360); Hypotonia (HP:0001252); Joint hypermobility (HP:0001382); Recurrent otitis media (HP:0000403); Bilateral cryptorchidism (HP:0008689); Attention deficit hyperactivity disorder (HP:0007018); Tall stature (HP:0000098); Delayed speech and language development (HP:0000750); Broad-based gait (HP:0002136); Pes planus (HP:0001763); Tented upper lip vermilion (HP:0010804); Broad nasal tip (HP:0000455); Preauricular pit (HP:0004467); Feeding difficulties (HP:0011968); Inguinal hernia (HP:0000023); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Constipation (HP:0002019); excluded: Attention deficit hyperactivity disorder (HP:0007018); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539) |
Individual 84 (MALE; P1Y2M) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.3281C>A (heterozygous) | Motor delay (HP:0001270); Large for gestational age (HP:0001520); Delayed speech and language development (HP:0000750); Torticollis (HP:0000473); Protruding ear (HP:0000411); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Seizure (HP:0001250); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539); excluded: Feeding difficulties (HP:0011968) |
Individual 85 (MALE; P33Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.3281C>A (heterozygous) | Specific learning disability (HP:0001328); Obesity (HP:0001513); Delayed speech and language development (HP:0000750); Protruding ear (HP:0000411); Tinnitus (HP:0000360); Hypertension (HP:0000822); excluded: Autistic behavior (HP:0000729); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539); excluded: Feeding difficulties (HP:0011968) |
Individual 4 (MALE; P14Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4696C>A (heterozygous) | Motor delay (HP:0001270); Intellectual disability, moderate (HP:0002342); Autistic behavior (HP:0000729); Attention deficit hyperactivity disorder (HP:0007018); Delayed speech and language development (HP:0000750); Delayed CNS myelination (HP:0002188); Depressed nasal bridge (HP:0005280); Macrodontia (HP:0001572); Low-set ears (HP:0000369); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539) |
Individual 10 (MALE; P4Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.3762_3764del (heterozygous) | Motor delay (HP:0001270); Autistic behavior (HP:0000729); Hypotonia (HP:0001252); Joint hypermobility (HP:0001382); Delayed speech and language development (HP:0000750); Global developmental delay (HP:0001263); Bruxism (HP:0003763); Relative macrocephaly (HP:0004482); Micrognathia (HP:0000347); Glossoptosis (HP:0000162); Cleft palate (HP:0000175); Feeding difficulties (HP:0011968); excluded: Sleep abnormality (HP:0002360); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539) |
Individual 34 (MALE; P11Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4118T>C (heterozygous) | Motor delay (HP:0001270); Intellectual disability, mild (HP:0001256); Autistic behavior (HP:0000729); Constipation (HP:0002019); Attention deficit hyperactivity disorder (HP:0007018); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Delayed speech and language development (HP:0000750); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539); excluded: Feeding difficulties (HP:0011968) |
Individual 38 (MALE; P6Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4193C>A (heterozygous) | Motor delay (HP:0001270); Autistic behavior (HP:0000729); Joint hypermobility (HP:0001382); Hypertension (HP:0000822); Delayed speech and language development (HP:0000750); Soft skin (HP:0000977); Synophrys (HP:0000664); Broad forehead (HP:0000337); Long uvula (HP:0010810); Feeding difficulties (HP:0011968); Hypotonia (HP:0001252); Joint laxity (HP:0001388); excluded: Sleep abnormality (HP:0002360); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Aggressive behavior (HP:0000718); excluded: Psychosis (HP:0000709); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539) |
Individual 44 (DDD_286674) (FEMALE; P3Y) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4724G>C (heterozygous) | Motor delay (HP:0001270); Hyperactivity (HP:0000752); Delayed speech and language development (HP:0000750); Malar flattening (HP:0000272); Prominent forehead (HP:0011220); Upslanted palpebral fissure (HP:0000582); Feeding difficulties (HP:0011968); Ketosis (HP:0001946); excluded: Autistic behavior (HP:0000729); excluded: Sleep abnormality (HP:0002360); excluded: Hypotonia (HP:0001252); excluded: Spasticity (HP:0001257); excluded: Syndactyly (HP:0001159); excluded: Pectus excavatum (HP:0000767); excluded: Strabismus (HP:0000486); excluded: Recurrent otitis media (HP:0000403); excluded: Constipation (HP:0002019); excluded: Hyperactivity (HP:0000752); excluded: Seizure (HP:0001250); excluded: Dystonia (HP:0001332); excluded: Scoliosis (HP:0002650); excluded: Cleft palate (HP:0000175); excluded: Abnormality of refraction (HP:0000539) |
Individual 49 (DEASD_0146_001) (MALE; P7Y3M) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4174G>A (heterozygous) | Motor delay (HP:0001270); Autistic behavior (HP:0000729); Macrocephaly (HP:0000256); Delayed speech and language development (HP:0000750); Enuresis (HP:0000805); excluded: Aggressive behavior (HP:0000718) |
Individual 50 (DEASD_0129_001) (MALE; P8Y7M) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4186T>A (heterozygous) | Autistic behavior (HP:0000729); excluded: Motor delay (HP:0001270); excluded: Delayed speech and language development (HP:0000750) |
Individual 54 (SSC_13675.p1) (MALE; n/a) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4187_4189del (heterozygous) | Autistic behavior (HP:0000729); Macrocephaly (HP:0000256) |
Individual 58 (DDD_305030) (MALE; n/a) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4187_4189del (heterozygous) | Motor delay (HP:0001270); Autistic behavior (HP:0000729); Delayed speech and language development (HP:0000750); Global developmental delay (HP:0001263); Brachycephaly (HP:0000248); Downslanted palpebral fissures (HP:0000494); Low-set ears (HP:0000369) |
Individual 59 (DDD_306396) (MALE; n/a) | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities (OMIM:618505) | NM_001080424.2:c.4222T>C (heterozygous) | Motor delay (HP:0001270); Hypotonia (HP:0001252); 2-3 toe syndactyly (HP:0004691); Delayed speech and language development (HP:0000750); Mild global developmental delay (HP:0011342); Dolichocephaly (HP:0000268); Unsteady gait (HP:0002317); Talipes (HP:0001883); Frontal bossing (HP:0002007); Prominent forehead (HP:0011220); excluded: 2-3 toe syndactyly (HP:0004691) |